Anomalia de Ebstein com coarctaçäo de aorta: uma associaçäo rara / Ebstein's anomaly with coarctation of the aorta: an unusual association
Arq. bras. cardiol
; 73(2): 219-24, ago. 1999. ilus
Article
in Pt, En
| LILACS
| ID: lil-252841
Responsible library:
BR1.1
RESUMO
Ebstein's anomaly with coarctation of the aorta is an extremely unusual condition. In this report, the clinical and surgical features of 3 male patients, aged 7 months, 4 years and 14 years, are discussed. All patients were in situs solittus. The first 2 patients had atrioventricular and ventriculoarterial discordance and progressed to heart failure in the neonatal period. The third had atrioventricular and ventriculoarterial concordance, as well as Wolf-Parkinson-White syndrome, with frequent episodes of paroxysmal tachycardia. The 3 patients underwent surgery for correction of the coarctation of the aorta. The patient with atrioventricular and ventriculoarterial concordance underwent tricuspid valvuloplasty using a De Vega-like technique. In addition, ablation of 2 anomalous pathways (Kent bundle), which were detected by the electrophysiologic study, was also subsequently performed. The 3 patients showed a good postoperative outcome for 2 years, although, in those with discordance, the surgical procedure did not influence the dysplasia of the tricuspid valve, because this valve showed light to moderate dysfunction.
Full text:
1
Index:
LILACS
Main subject:
Aortic Coarctation
/
Ebstein Anomaly
Type of study:
Diagnostic_studies
/
Risk_factors_studies
Limits:
Adolescent
/
Child, preschool
/
Humans
/
Infant
/
Male
Language:
En
/
Pt
Journal:
Arq. bras. cardiol
Journal subject:
CARDIOLOGIA
Year:
1999
Type:
Article