Your browser doesn't support javascript.
loading
Anomalia de Ebstein com coarctaçäo de aorta: uma associaçäo rara / Ebstein's anomaly with coarctation of the aorta: an unusual association
Ebaid, Mun; Azeka, Estela; Ikari, Nana Miura; Sosa, Eduardo A; Marcial, Miguel Barbero; Atik, Edmar.
Affiliation
  • Ebaid, Mun; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto do Coraçäo.
  • Azeka, Estela; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto do Coraçäo.
  • Ikari, Nana Miura; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto do Coraçäo.
  • Sosa, Eduardo A; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto do Coraçäo.
  • Marcial, Miguel Barbero; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto do Coraçäo.
  • Atik, Edmar; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto do Coraçäo.
Arq. bras. cardiol ; 73(2): 219-24, ago. 1999. ilus
Article in Pt, En | LILACS | ID: lil-252841
Responsible library: BR1.1
RESUMO
Ebstein's anomaly with coarctation of the aorta is an extremely unusual condition. In this report, the clinical and surgical features of 3 male patients, aged 7 months, 4 years and 14 years, are discussed. All patients were in situs solittus. The first 2 patients had atrioventricular and ventriculoarterial discordance and progressed to heart failure in the neonatal period. The third had atrioventricular and ventriculoarterial concordance, as well as Wolf-Parkinson-White syndrome, with frequent episodes of paroxysmal tachycardia. The 3 patients underwent surgery for correction of the coarctation of the aorta. The patient with atrioventricular and ventriculoarterial concordance underwent tricuspid valvuloplasty using a De Vega-like technique. In addition, ablation of 2 anomalous pathways (Kent bundle), which were detected by the electrophysiologic study, was also subsequently performed. The 3 patients showed a good postoperative outcome for 2 years, although, in those with discordance, the surgical procedure did not influence the dysplasia of the tricuspid valve, because this valve showed light to moderate dysfunction.
Subject(s)
Full text: 1 Index: LILACS Main subject: Aortic Coarctation / Ebstein Anomaly Type of study: Diagnostic_studies / Risk_factors_studies Limits: Adolescent / Child, preschool / Humans / Infant / Male Language: En / Pt Journal: Arq. bras. cardiol Journal subject: CARDIOLOGIA Year: 1999 Type: Article
Full text: 1 Index: LILACS Main subject: Aortic Coarctation / Ebstein Anomaly Type of study: Diagnostic_studies / Risk_factors_studies Limits: Adolescent / Child, preschool / Humans / Infant / Male Language: En / Pt Journal: Arq. bras. cardiol Journal subject: CARDIOLOGIA Year: 1999 Type: Article