Amiloidose traqueobrônquica primária / Primary tracheobronchial amyloidosis
J. bras. pneumol
; 34(10): 881-884, out. 2008. ilus
Article
in En, Pt
| LILACS
| ID: lil-496621
Responsible library:
BR1.1
ABSTRACT
Tracheobronchial amyloidosis is an uncommon localized form of amyloidosis, characterized by amyloid deposits restricted to the trachea, main bronchi and segmental bronchi. We present the case of a retired 67-year-old man with long-term progressive dyspnea, wheezing and chest pain. A diagnosis of tracheobronchial amyloidosis was made after the third fiberoptic bronchoscopy and histological confirmation through Congo red staining of tissue samples.
RESUMO
A amiloidose traqueobrônquica é uma forma pouco comum de amiloidose localizada, caracterizada por depósitos amilóides limitados à traquéia, brônquios principais e brônquios segmentares. Nós apresentamos o caso de um homem aposentado de 67 anos com dispnéia progressiva de longa data, sibilância e dor torácica. O diagnóstico de amiloidose traqueobrônquica foi realizado após três fibrobroncoscopias e confirmação histopatológica com coloração vermelho congo.
Key words
Full text:
1
Index:
LILACS
Main subject:
Tracheal Diseases
/
Bronchial Diseases
/
Amyloidosis
Type of study:
Diagnostic_studies
/
Etiology_studies
Limits:
Humans
/
Male
Language:
En
/
Pt
Journal:
J. bras. pneumol
Journal subject:
PNEUMOLOGIA
Year:
2008
Type:
Article