Mielopatia associada ao HTLV-I: aspectos relacionados à infância / HTLV-I associated myelopathy: aspects related to childhood
Rev. bras. neurol
;
45(2): 41-46, abr.-jun. 2009.
Article
in Portuguese
| LILACS
| ID: lil-518014
RESUMO
A mielopatia associada ao HTLV-I ou paraparesia espástica tropical (HAM/TSP) é caracterizada por uma paraparesia espástica lentamente progressiva associada a disfunções esfincterianas e sensitivas. A enfermidade acomete indivíduos na faixa etária dos 30 aos 50 anos, sendo um diagnóstico negligenciado em crianças que se apresentam com paraparesia espástica de curso evolutivo. O presente estudo propõe uma revisão dos aspectos clínicos e epidemiológicos relacionados à HAM/TSP, suas principais formas de transmissão e os critérios para o diagnóstico em crianças com queixas neurológicas sugestivas.O conhecimento detalhado dos aspectos clínicos e laboratoriais que definem tal condição na infância e na adolescência contribui para o diagnóstico precoce desta enfermidade neurológica incapacitante.
ABSTRACT
The HTLV-I-associated myelopathy or tropical spastic paraparesis (HAM/TSP) is characterized by a slowly progressive spastic paraparesis associated with sphincter and sensory dysfunction. The disorder usually affects people aged from 30 to 50 years. This diagnosis is neglected by many clinicians in children who present with spastic paraparesis of progressive course. This study proposes a revision of clinical and epidemiological aspects related to HAM/TSP in children, their main mechanisms of transmission and the diagnosis criteria with suggestive neurological complaints. The detailed knowledge of clinical and laboratory that define this condition in childhood and adolescence will help to early diagnosis of this disabling neurological illness.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Blood Transfusion
/
Breast Feeding
/
Paraparesis, Tropical Spastic
/
Infectious Disease Transmission, Vertical
Type of study:
Risk factors
/
Screening study
Limits:
Adolescent
/
Child
/
Female
/
Humans
/
Male
Country/Region as subject:
South America
/
Brazil
Language:
Portuguese
Journal:
Rev. bras. neurol
Journal subject:
Neurology
Year:
2009
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Universidade Federal do Estado do Rio de Janeiro/BR
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