Surgical treatment of primary cardiac rhabdomyosarcoma / Tratamento cirúrgico de rabdomiosarcoma primário do coração
Rev. bras. cir. cardiovasc
; 24(2): 242-244, abr.-jun. 2009. ilus
Article
in En
| LILACS
| ID: lil-525557
Responsible library:
BR1.1
ABSTRACT
The authors report a case of a 16-year-old man who presented progressive dyspnea. At that time the diagnosis of rheumatic fever with mitral valve involvement was performed. The bidimensional echocardiogram showed presence of mobile mass inside the left atrium. The tumor presented lobules, projecting into the left ventricle during the diastole and provoking turbulence. The patient underwent surgical resection with postoperative course needing re-operation for mitral valve replacement. Histopathology has proven that such tumor was a primary cardiac rhabdomyosarcoma and the early clinical diagnosis of rheumatic mitral valve disease was very difficult.
RESUMO
Os autores reportam caso de jovem de 16 anos, o qual apresentou dispnéia progressiva. No momento do atendimento foi feito diagnóstico de febre reumática com comprometimento da valva mitral. Ecocardiograma bidimensional demonstrou a presença de massa móvel dentro do átrio esquerdo. O tumor apresentava lobos, se projetando para o interior do ventrículo esquerdo durante a diástole, provocando turbulência. O paciente foi submetido a ressecção cirúrgica, complicada com reoperação e troca valvar mitral. A histopatologia demonstrou tratar-se de rabdomiosarcoma primário e o diagnóstico clínico diferencial com febre reumática e doença valvar mitral foi muito difícil desde o seu início.
Key words
Full text:
1
Index:
LILACS
Main subject:
Rhabdomyosarcoma
/
Heart Neoplasms
/
Mitral Valve
/
Mitral Valve Stenosis
Type of study:
Diagnostic_studies
Limits:
Adolescent
/
Humans
/
Male
Language:
En
Journal:
Rev. bras. cir. cardiovasc
Journal subject:
CARDIOLOGIA
/
CIRURGIA GERAL
Year:
2009
Type:
Article