A raridade histológica no câncer da tireoide / The histological rarity of thyroid cancer
Braz. j. otorhinolaryngol. (Impr.)
;
78(4): 48-51, jul.-ago. 2012. ilus, tab
Article
in Portuguese
| LILACS
| ID: lil-646770
RESUMO
O câncer da tireoide é a neoplasia endócrina mais comum, correspondendo a cerca de 1% de todos os tipos de câncer. Sarcomas, linfomas e metástases para a glândula tireoide são raros e pouco descritos na literatura. OBJETIVO:
Descrever tipos histológicos raros de câncer de tireoide em serviço de referência.MÉTODOS:
Revisão de prontuários de pacientes admitidos com diagnóstico de câncer de tireoide no período de 1977 a 2010. Foram coletadas informações demográficas, diagnósticas, terapêuticas e histopatológicas.RESULTADOS:
Foram revisados 3018 prontuários de pacientes admitidos com doença tireoidiana. Dos casos com diagnóstico de tumores raros, predominou o tipo histológico carcinoma anaplásico, com 22 casos (0,7%), seguido por 11 casos de carcinoma medular (0,36%), dois de sarcoma (0,07%), dois de linfoma (0,07%) e um de tumor carcinoide metastático (0,03%). Houve predomínio do gênero feminino (57%) e de caucasianos (84%). A apresentação clínica com nódulo tireoídeo palpável foi a mais frequente. Todos os casos de linfoma, sarcoma e carcinoma anaplásico evoluíram a óbito.CONCLUSÃO:
Sarcomas, linfomas e metástases em tireoide são incomuns e tendem à evolução desfavorável.ABSTRACT
Thyroid cancer is the most common endocrine cancer, accounting for about 1% of all cancers. Sarcomas, lymphomas and metastases to the thyroid gland are rare and only with a handful of descriptions in the literature. OBJECTIVE:
To describe rare histological types of thyroid cancer found in a reference center.METHODS:
Medical chart review from admitted patients diagnosed with thyroid cancer in the period from 1977 to 2010. Demographic, diagnostic, therapeutic and histopathological information were collected.RESULTS:
3,018 records of patients admitted with thyroid disease were reviewed. Among the cases diagnosed with rare tumors there was a predominance of anaplastic carcinoma 22 cases (0.7%), followed by 11 cases of medullary carcinoma (0.36%); 2 cases of sarcoma (0.07%), 2 cases of lymphoma (0.07%) and one case of metastatic carcinoid tumor (0.03%). There were more females diagnosed (57%) as well as Caucasians (84%). The most frequent clinical presentation was a palpable thyroid nodule. All patients with lymphoma, sarcoma and anaplastic carcinoma died.CONCLUSION:
Sarcomas, lymphomas and thyroid metastases are uncommon and tend to worse outcomes.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Sarcoma
/
Thyroid Neoplasms
/
Carcinoma
/
Rare Diseases
/
Lymphoma
Type of study:
Observational study
Limits:
Female
/
Humans
/
Male
Language:
Portuguese
Journal:
Braz. j. otorhinolaryngol. (Impr.)
Journal subject:
Otolaryngology
Year:
2012
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Hospital Heliópolis/BR
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