The case of a boy with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita: a unique instance of phacomatosis pigmentovascularis
An. bras. dermatol
; An. bras. dermatol;90(3,supl.1): 10-12, May-June 2015. tab, ilus
Article
in En
| LILACS
| ID: lil-755755
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BR1.1
ABSTRACT
Phacomatosis pigmentovascularis is a rare, congenital condition characterized by a combination of cutaneous melanocytic lesions and vascular malformation. We discuss an entirely unique case of Phacomatosis pigmentovascularis with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita, which may represent a heretofore undescribed variant of phacomatosis pigmentovascularis.
.Key words
Full text:
1
Index:
LILACS
Main subject:
Skin Neoplasms
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Telangiectasis
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Nevus of Ota
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Skin Diseases, Vascular
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Port-Wine Stain
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Neurocutaneous Syndromes
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Mongolian Spot
Limits:
Humans
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Male
Language:
En
Journal:
An. bras. dermatol
Journal subject:
DERMATOLOGIA
Year:
2015
Type:
Article