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Segmental Darier's disease: a presentation of difficult diagnosis
Medeiros, Paula Mota; Alves, Natália Ribeiro de Magalhães; Trujillo, Jeniffer Muñoz; Silva, Cássia Camarinha da; Faria, Paula Carolina Pessanha de; Silva, Roberto Souto da.
Affiliation
  • Medeiros, Paula Mota; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
  • Alves, Natália Ribeiro de Magalhães; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
  • Trujillo, Jeniffer Muñoz; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
  • Silva, Cássia Camarinha da; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
  • Faria, Paula Carolina Pessanha de; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
  • Silva, Roberto Souto da; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
An. bras. dermatol ; 90(3,supl.1): 62-65, May-June 2015. ilus
Article in En | LILACS | ID: lil-755778
Responsible library: BR1.1
ABSTRACT
Abstract

Darier's disease is a rare autosomal dominant genodermatosis. It has an estimated prevalence of 1 in 55,000 to 100,000 individuals, regardless of gender. It is characterized by multiple keratotic papules on the seborrheic areas of the trunk, scalp, forehead and flexures, and the clinical picture is worsened by heat, sun exposure, perspiration and mechanical trauma. Histopathology observed loss of epithelial adhesion and abnormal keratinization. About 10% of cases present in the localized form of the disease. We report a case of segmental Darier's Disease Type I and discuss the main characteristics of this condition.

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Full text: 1 Index: LILACS Main subject: Darier Disease Type of study: Diagnostic_studies / Risk_factors_studies Limits: Adult / Female / Humans Language: En Journal: An. bras. dermatol Journal subject: DERMATOLOGIA Year: 2015 Type: Article

Full text: 1 Index: LILACS Main subject: Darier Disease Type of study: Diagnostic_studies / Risk_factors_studies Limits: Adult / Female / Humans Language: En Journal: An. bras. dermatol Journal subject: DERMATOLOGIA Year: 2015 Type: Article