Segmental Darier's disease: a presentation of difficult diagnosis
An. bras. dermatol
; 90(3,supl.1): 62-65, May-June 2015. ilus
Article
in En
| LILACS
| ID: lil-755778
Responsible library:
BR1.1
ABSTRACT
Darier's disease is a rare autosomal dominant genodermatosis. It has an estimated prevalence of 1 in 55,000 to 100,000 individuals, regardless of gender. It is characterized by multiple keratotic papules on the seborrheic areas of the trunk, scalp, forehead and flexures, and the clinical picture is worsened by heat, sun exposure, perspiration and mechanical trauma. Histopathology observed loss of epithelial adhesion and abnormal keratinization. About 10% of cases present in the localized form of the disease. We report a case of segmental Darier's Disease Type I and discuss the main characteristics of this condition.
.Key words
Full text:
1
Index:
LILACS
Main subject:
Darier Disease
Type of study:
Diagnostic_studies
/
Risk_factors_studies
Limits:
Adult
/
Female
/
Humans
Language:
En
Journal:
An. bras. dermatol
Journal subject:
DERMATOLOGIA
Year:
2015
Type:
Article