Peutz-jeghers syndrome and colon cancer in a 10-year-old girl: implications for when and how to start screening?
Article
in English
| IMSEAR
| ID: sea-37667
ABSTRACT
The Peutz-Jeghers syndrome (PJS) is characterized by hamartomatous polyposis of the gastro-intestinal (GI) tract, with mucocutaneous pigmentation. We have experienced a case of a 10-year-old girl who presented with PJS, intussusception, colonic perforation and colonic adenocarcinoma. Finally, this case developed airway obstruction from the mediastinal mass. In order to prevent cancer and short bowel syndrome, aggressive screening is recommended.
Full text:
Available
Index:
IMSEAR (South-East Asia)
Main subject:
Female
/
Humans
/
Peutz-Jeghers Syndrome
/
Adenocarcinoma
/
Child
/
Colonic Neoplasms
/
Fatal Outcome
/
Airway Obstruction
Type of study:
Diagnostic study
/
Screening study
Language:
English
Year:
2008
Type:
Article
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