Wunderlich's syndrome with hepatic angiomyolipoma in tuberous sclerosis.
Indian J Cancer
; 2008 Apr-Jun; 45(2): 64-6
Article
in En
| IMSEAR
| ID: sea-50255
ABSTRACT
We present a patient of tuberous sclerosis complex with bilateral renal angiomyolipoma and hepatic angiomyolipoma with spontaneous retroperitoneal hemorrhage from right angiomyolipoma (Wunderlich's syndrome). Nephron preserving approach was tried but the right kidney could not be salvaged. Hepatic angiomyolipoma was managed conservatively. Wunderlich's syndrome has been found in around 10% of cases of renal angiomyolipomas. Hepatic Angiomyolipoma is a benign mesenchymal neoplasm of the liver which is rarely reported in literature.
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Language:
En
Journal:
Indian J Cancer
Year:
2008
Type:
Article