A Case of Churg-Strauss Syndrome with Interstinal Perforation / 결핵및호흡기질환
Tuberculosis and Respiratory Diseases
; : 374-379, 2009.
Article
in Ko
| WPRIM
| ID: wpr-28800
Responsible library:
WPRO
ABSTRACT
Churg-Strauss syndrome (CSS) or allergic granulomatous angiitis is a rare syndrome that is characterized by hypereosinophilic systemic necrotizing vasculitis affecting small- to medium-sized arteries and veins. In general, it occurs in individuals with pre-existing allergic asthma. When CSS appears in patients, it has the following characteristics eosinophilia of more than 10% in peripheral blood, paranasal sinusitis, pulmonary infiltrates, histological proof of vasculitis with extravascular eosinophils, and mononeuritis multiplex or polyneuropathy. Therapeutic trials dedicated to Churg-Strauss syndrome have been limited due to the rarity of this disorder and the difficulty in making a histological diagnosis. Proper treatment of patients with CSS is not widely known. In this case study, we report on our experience with an unusual patient case, characterized by purpura and a perforation of the small intestine after inadequate steroid therapy.
Key words
Full text:
1
Index:
WPRIM
Main subject:
Polyneuropathies
/
Arteries
/
Purpura
/
Asthma
/
Sinusitis
/
Vasculitis
/
Veins
/
Churg-Strauss Syndrome
/
Mononeuropathies
/
Eosinophilia
Limits:
Humans
Language:
Ko
Journal:
Tuberculosis and Respiratory Diseases
Year:
2009
Type:
Article