Pathological morphology and surgical treatment of cor triatriatum associated with deformities / 中华胸心血管外科杂志

ABSTRACT

Ovbective To summarize the clinic data of pathological morphology,diagnosis,surgical treatment and associated anomalies of cor triatriatum from 37 patients enlisted in this study. Methods Thirty-seven patients,21 males and 16 females with a mean age of (9.8?8.6) years were studied. Clinical pathologic anatomy of cor triatriatum was type I in 2 cases,type IIa in 9,type IIb in 24,and type III in 2. Complete cor triatriatum in 31 cases and incomplete cor triatriatum in 6. Thirty-two cases (86%) accompanied with other cardiovascular anomalies. Diagnosis was made in 16(43%) cases preoperatively. All patients had excision of the fibromuscular membrane through the right atrial transseptal approach. Results The mortality rate in this group was 8.11% (3 of 37 cases). Thirty-four cases were followed up after surgery from 3 months to 15 years was satisfactory. Conclusion Cor triatriatum is a rare congenital cardiac anomaly. Treatment of associated deformities was a committed step in cor triatriatum surgical correction. Result of surgical treatment was satisfactory.