A Case of Glanzmann's Thrombasthenia Successfully Managed after Tonsillectomy / 임상소아혈액종양
Clinical Pediatric Hematology-Oncology
; : 29-32, 2014.
Article
in En
| WPRIM
| ID: wpr-788505
Responsible library:
WPRO
ABSTRACT
Glanzmann's thrombasthenia (GT) is a rare autosomal recessive disease and platelet function disorder, in which platelet membrane GP IIb/ IIIa complex is defective and platelet aggregation is undeveloped. GT is characterized by mucocutaneous hemorrhages, such as, epistaxis, purpura, gingival bleeding, and menorrhagia, severe bleeding complications during surgery. We report the case of a 6-year-old boy with GT who underwent tonsillectomy. Here, we focus on perioperative hemostatic management using recombinant factor VIIa, fibrin glue and hemostat materials.
Key words
Full text:
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Index:
WPRIM
Main subject:
Purpura
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Tonsillectomy
/
Blood Platelets
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Thrombasthenia
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Factor VIIa
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Fibrin Tissue Adhesive
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Platelet Aggregation
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Epistaxis
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Hemorrhage
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Hemostasis
Limits:
Child
/
Female
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Humans
/
Male
Language:
En
Journal:
Clinical Pediatric Hematology-Oncology
Year:
2014
Type:
Article