A Case of adrenocortical oncocytoma Presenting with Peripheral Precocious Puberty
Annals of Pediatric Endocrinology & Metabolism
; : 49-52, 2012.
Article
in Ko
| WPRIM
| ID: wpr-89109
Responsible library:
WPRO
ABSTRACT
Adrenocortical oncocytoma is a rare adrenal gland tumor, and in most cases, benign and non-functioning. Functional adrenocortical oncocytoma has only been reported in eleven cases worldwide, including three children. These cases all showed clinical symptoms and signs, such as virilization, feminization, Cushing syndrome and Conn syndrome, as a result of overproduction of adrenal steroid hormones. We report a 2-year-old girl who presented with precocious puberty with premature pubarche. Dehydroepiandrosterone sulfate (DHEA-S) and testosterone levels were elevated and a 1.9 cm right adrenocortical oncocytoma was found. After tumor resection, her hormone levels were normalized.
Key words
Full text:
1
Index:
WPRIM
Main subject:
Puberty, Precocious
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Testosterone
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Virilism
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Child, Preschool
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Adrenal Glands
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Adenoma, Oxyphilic
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Dehydroepiandrosterone Sulfate
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Cushing Syndrome
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Feminization
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Hyperaldosteronism
Limits:
Child
/
Humans
Language:
Ko
Journal:
Annals of Pediatric Endocrinology & Metabolism
Year:
2012
Type:
Article