A Case of Essential Iris Atrophy

ABSTRACT

Essential iris atrophy is a disease characterized by corectopia, iris atrophy, iris hole formation, corneal endothelial degeneration, peripheral anterior synechia, and glaucoma. This disease shares common properties with Chandler's syndrome and Cogan-Reese syndrome, so above three diseases are catagorized by iridocorneal endothelial(ICE) syndrome. We have experienced a patient who had a complaint of visual dimness in right eye. On examination, she had corectopia, iris hole and atrophy, and increased IOP in right eye. Specular microscopic finding was consistent with essential iris atrophy.