Assuntos
Artrite Reumatoide/complicações , Artrite Reumatoide/diagnóstico , Linfoma Cutâneo de Células T/complicações , Linfoma Cutâneo de Células T/diagnóstico , Neoplasias Cutâneas/complicações , Neoplasias Cutâneas/diagnóstico , Adulto , Artrite Reumatoide/terapia , Humanos , Linfoma Cutâneo de Células T/terapia , Masculino , Neoplasias Cutâneas/terapiaAssuntos
Corticosteroides/administração & dosagem , Linfócitos T CD4-Positivos , Interleucinas/administração & dosagem , Linfoma Cutâneo de Células T/tratamento farmacológico , Transtornos Linfoproliferativos/tratamento farmacológico , Neoplasias Cutâneas/tratamento farmacológico , Adulto , Feminino , Humanos , Injeções Intralesionais/métodos , Linfoma Cutâneo de Células T/complicações , Linfoma Cutâneo de Células T/diagnóstico , Transtornos Linfoproliferativos/complicações , Transtornos Linfoproliferativos/diagnóstico , Nariz/efeitos dos fármacos , Nariz/patologia , Neoplasias Cutâneas/complicações , Neoplasias Cutâneas/diagnósticoRESUMO
Subcutaneous panniculitis-like T cell lymphoma is a rare subtype of cutaneous lymphomas with distinct clinical, histological and immunophenotypic characteristics, as well as an indolent clinical course. Rarely, it may be complicated with hemophagocytic lymphohistiocytosis: a hyperinflammatory syndrome which, if not diagnosed early, carries a dismal outcome. In this article, we describe a case of subcutaneous panniculitis-like T cell lymphoma in a middle-aged female patient which was complicated with secondary hemophagocytic lymphohistiocytosis with a favorable outcome following etoposide-based therapy. The various histological mimics of subcutaneous panniculitis-like T cell lymphoma and the management options are also briefly discussed.
Assuntos
Linfo-Histiocitose Hemofagocítica/diagnóstico , Linfoma Cutâneo de Células T/diagnóstico , Paniculite/diagnóstico , Neoplasias Cutâneas/diagnóstico , Adulto , Feminino , Humanos , Linfo-Histiocitose Hemofagocítica/complicações , Linfoma Cutâneo de Células T/complicações , Paniculite/complicações , Neoplasias Cutâneas/complicaçõesAssuntos
Células Matadoras Naturais/patologia , Linfoma Cutâneo de Células T/diagnóstico , Neoplasias Cutâneas/diagnóstico , Idoso , Feminino , Humanos , Células Matadoras Naturais/imunologia , Linfoma Cutâneo de Células T/complicações , Linfoma Cutâneo de Células T/imunologia , Neoplasias Cutâneas/complicações , Neoplasias Cutâneas/imunologiaRESUMO
Natural killer/T-cell lymphoma is a rare, Epstein-Barr virus-associated type of cytotoxic lymphoma thatpresents mainly in the nasal cavity and its vicinity. Very few cases of primary cutaneous extranodal natural killer/T-cell lymphoma have been reported till date. All the previously reported cases of primary cutaneous extranodalnatural killer/T-cell lymphoma presented as lesions resembling cellulitis, subcutaneous nodules or ulcers. We report a rare case which presented as erythematous and purpuric round patches on the arms and was finally diagnosed as primary cutaneous extranodalnatural killer/T-cell lymphoma, following a skin biopsy. The atypical patchy lesions presented a diagnostic challenge. We herein describe this clinically novel atypical patch-like presentation of primary cutaneous extranodalnatural killer/T-cell lymphoma together with the key histopathologic features and highlights of the previously reported cases.