RESUMO
We report here the case of a 17 year-old girl with the classic signs of Goldenhar syndrome in the form of multiple accessory tragi, bilateral ocular dermoids, mandibular hypoplasia (micrognathia) and cervical lordosis. She also had a high arched palate, gingival hypertrophy and malaligned teeth, features which are as yet unreported.
Assuntos
Anormalidades Múltiplas/patologia , Síndrome de Goldenhar/patologia , Adolescente , Coristoma/patologia , Cisto Dermoide/patologia , Pavilhão Auricular , Neoplasias Oculares/patologia , Feminino , Hipertrofia Gengival/patologia , Humanos , Palato/anormalidades , Dermatopatias/patologia , Anormalidades Dentárias/patologiaRESUMO
We describe a 50-year-old man with a 10-year history of gradually enlarging limbal tumors and conjunctival injection. An excised limbal mass presented a diagnostic challenge histopathologically and was initially believed to be a fibrous histiocytoma. Special stains, however, revealed acid-fast organisms in the fibrous histiocytes, and the diagnosis was changed to corneal leproma. This case confirms the existence of fibrous histiocytoma-like lesions in leprosy, which in this form can be termed fibrous histiocytoid leprosy. Furthermore, it suggests the need for special stains to rule out infectious cause in lesions believed to be atypical fibrous histiocytomas.