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1.
The first knock-in rat model for glutaric aciduria type I allows further insights into pathophysiology in brain and periphery.
Mol Genet Metab
; 133(2): 157-181, 2021 06.
Article
in English
| MEDLINE | ID: mdl-33965309
2.
Ammonium accumulation and chemokine decrease in culture media of Gcdh-/- 3D reaggregated brain cell cultures.
Mol Genet Metab
; 126(4): 416-428, 2019 04.
Article
in English
| MEDLINE | ID: mdl-30686684
3.
New in vitro model derived from brain-specific Mut-/- mice confirms cerebral ammonium accumulation in methylmalonic aciduria.
Mol Genet Metab
; 124(4): 266-277, 2018 08.
Article
in English
| MEDLINE | ID: mdl-29934063
4.
Ammonium accumulation is a primary effect of 2-methylcitrate exposure in an in vitro model for brain damage in methylmalonic aciduria.
Mol Genet Metab
; 119(1-2): 57-67, 2016 09.
Article
in English
| MEDLINE | ID: mdl-27599447
5.
Immunolocalization of glutaryl-CoA dehydrogenase (GCDH) in adult and embryonic rat brain and peripheral tissues.
Neuroscience
; 343: 355-363, 2017 02 20.
Article
in English
| MEDLINE | ID: mdl-27984186
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