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1.
Receptor-mediated activation of CFTR via prostaglandin signaling pathways in the airway.
Am J Physiol Lung Cell Mol Physiol
; 322(3): L305-L314, 2022 03 01.
Article
in English
| MEDLINE | ID: mdl-35020527
2.
Characterizing mucociliary clearance in young children with cystic fibrosis.
Pediatr Res
; 91(3): 612-620, 2022 02.
Article
in English
| MEDLINE | ID: mdl-33753897
3.
The Changing Face of Cystic Fibrosis: An Update for Anesthesiologists.
Anesth Analg
; 134(6): 1245-1259, 2022 06 01.
Article
in English
| MEDLINE | ID: mdl-35020677
4.
Airway microbiota across age and disease spectrum in cystic fibrosis.
Eur Respir J
; 50(5)2017 11.
Article
in English
| MEDLINE | ID: mdl-29146601
5.
6.
Clinical Phenotypes and Genotypic Spectrum of Cystic Fibrosis in Chinese Children.
J Pediatr
; 171: 269-76.e1, 2016 Apr.
Article
in English
| MEDLINE | ID: mdl-26826884
7.
Dual activation of CFTR and CLCN2 by lubiprostone in murine nasal epithelia.
Am J Physiol Lung Cell Mol Physiol
; 304(5): L324-31, 2013 Mar 01.
Article
in English
| MEDLINE | ID: mdl-23316067
8.
N-acetylcysteine enhances cystic fibrosis sputum penetration and airway gene transfer by highly compacted DNA nanoparticles.
Mol Ther
; 19(11): 1981-9, 2011 Nov.
Article
in English
| MEDLINE | ID: mdl-21829177
9.
Net benefit of ivacaftor during prolonged tezacaftor/elexacaftor exposure in vitro.
J Cyst Fibros
; 21(4): 637-643, 2022 07.
Article
in English
| MEDLINE | ID: mdl-35248469
10.
IL-13-programmed airway tuft cells produce PGE2, which promotes CFTR-dependent mucociliary function.
JCI Insight
; 7(13)2022 07 08.
Article
in English
| MEDLINE | ID: mdl-35608904
11.
Ubiquitin C-terminal hydrolase-L1 protects cystic fibrosis transmembrane conductance regulator from early stages of proteasomal degradation.
J Biol Chem
; 285(15): 11314-25, 2010 Apr 09.
Article
in English
| MEDLINE | ID: mdl-20147297
12.
Cystic fibrosis and estrogens: a perfect storm.
J Clin Invest
; 118(12): 3841-4, 2008 Dec.
Article
in English
| MEDLINE | ID: mdl-19033654
13.
Elexacaftor is a CFTR potentiator and acts synergistically with ivacaftor during acute and chronic treatment.
Sci Rep
; 11(1): 19810, 2021 10 06.
Article
in English
| MEDLINE | ID: mdl-34615919
14.
Measurements of spontaneous CFTR-mediated ion transport without acute channel activation in airway epithelial cultures after modulator exposure.
Sci Rep
; 11(1): 22616, 2021 11 19.
Article
in English
| MEDLINE | ID: mdl-34799640
15.
Downregulation of epithelial sodium channel (ENaC) activity in human airway epithelia after low temperature incubation.
BMJ Open Respir Res
; 8(1)2021 02.
Article
in English
| MEDLINE | ID: mdl-33622672
16.
Applications of proteomic technologies for understanding the premature proteolysis of CFTR.
Expert Rev Proteomics
; 7(4): 473-86, 2010 Aug.
Article
in English
| MEDLINE | ID: mdl-20653504
17.
Description of a standardized nutrition classification plan and its relation to nutritional outcomes in children with cystic fibrosis.
J Pediatr Psychol
; 35(1): 6-13, 2010.
Article
in English
| MEDLINE | ID: mdl-19420226
18.
Chemical rescue of deltaF508-CFTR mimics genetic repair in cystic fibrosis bronchial epithelial cells.
Mol Cell Proteomics
; 7(6): 1099-110, 2008 Jun.
Article
in English
| MEDLINE | ID: mdl-18285607
19.
Effect of apical chloride concentration on the measurement of responses to CFTR modulation in airway epithelia cultured from nasal brushings.
Physiol Rep
; 8(19): e14603, 2020 10.
Article
in English
| MEDLINE | ID: mdl-33038073
20.
Changes in mucociliary clearance over time in children with cystic fibrosis.
Pediatr Pulmonol
; 55(9): 2307-2314, 2020 09.
Article
in English
| MEDLINE | ID: mdl-32427408