Asunto(s)
Neoplasias de la Tiroides , Biomarcadores de Tumor , Femenino , Humanos , Inmunohistoquímica , Persona de Mediana Edad , Glándula Tiroides/patología , Neoplasias de la Tiroides/diagnóstico , Neoplasias de la Tiroides/diagnóstico por imagen , Neoplasias de la Tiroides/patología , UltrasonografíaAsunto(s)
Carcinoma de Células Renales/etiología , Enfermedades Renales Quísticas/complicaciones , Neoplasias Renales/etiología , Carcinoma de Células Renales/diagnóstico , Carcinoma de Células Renales/patología , Diagnóstico Diferencial , Humanos , Enfermedades Renales Quísticas/diagnóstico , Enfermedades Renales Quísticas/patología , Enfermedades Renales Quísticas/terapia , Fallo Renal Crónico/complicaciones , Fallo Renal Crónico/patología , Fallo Renal Crónico/terapia , Neoplasias Renales/diagnóstico , Neoplasias Renales/patología , Masculino , Persona de Mediana Edad , Diálisis Renal , UrografíaAsunto(s)
Neoplasias Gastrointestinales/diagnóstico , Tumores del Estroma Gastrointestinal/diagnóstico , Pólipos/diagnóstico , Neoplasias Gástricas/diagnóstico , Diagnóstico Diferencial , Progresión de la Enfermedad , Neoplasias Gastrointestinales/patología , Tumores del Estroma Gastrointestinal/patología , Humanos , Masculino , Persona de Mediana Edad , Pólipos/patología , Neoplasias Gástricas/patologíaRESUMEN
Amyloidosis is a rare disease that results from the extracellular deposition of amorphous fibrillar protein. It is usually observed in a systemic form. Gastrointestinal involvement is frequent but peritoneal localization is unusual. A 43-year-old male was investigated for nephritic colic. Morphologic explorations revealed small intestine agglomerans in the periumbilical region, infiltration of peritoneal fat and multiple coelio-mesenteric lymph nodes. There were no clinical or biological abnormalities and endoscopic examinations were normal. The patient then underwent an exploratory laparoscopy. Macroscopically false membranes were seen throughout the peritoneum and small bowel without ascites. Anatomopathologic examination diagnosed peritoneal amyloidosis. After several investigations a diagnosis of a primary peritoneal amyloidosis was confirmed. The patient was treated with melphalan and prednisone with a favorable outcome. Our case illustrates a particular presentation of peritoneal amyloidosis. Despite improved imaging methods, peritoneal biopsy remains essential for diagnosis.