GPs Meet Rare Lung Disorders Task Force factsheet: primary ciliary dyskinesia.
Breathe (Sheff)
; 11(2): 159-61, 2015 Jun.
Article
en En
| MEDLINE
| ID: mdl-26306119
ABSTRACT
Primary ciliary dyskinesia (PCD) is a rare, autosomal recessive disease of abnormalities of ciliary structure and function. The result is impaired mucociliary clearance, causing a variety of respiratory symptoms, and likely progression to bronchiectasis in most cases. Situs anomalies are present in nearly 50% of cases.
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Colección:
01-internacional
Banco de datos:
MEDLINE
Idioma:
En
Revista:
Breathe (Sheff)
Año:
2015
Tipo del documento:
Article