Report of two novel mutations in PTHLH associated with brachydactyly type E and literature review.
Am J Med Genet A
; 170(3): 734-42, 2016 Mar.
Article
en En
| MEDLINE
| ID: mdl-26640227
Autosomal-dominant brachydactyly type E is a congenital limb malformation characterized by small hands and feet as a result of shortened metacarpals and metatarsals. Alterations that predict haploinsufficiency of PTHLH, the gene coding for parathyroid hormone related protein (PTHrP), have been identified as a cause of this disorder in seven families. Here, we report three patients affected with brachydactyly type E, caused by PTHLH mutations expected to result in haploinsufficiency, and discuss our data compared to published reports.
Palabras clave
Texto completo:
1
Colección:
01-internacional
Banco de datos:
MEDLINE
Asunto principal:
Proteína Relacionada con la Hormona Paratiroidea
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Braquidactilia
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Mutación
Tipo de estudio:
Prognostic_studies
/
Risk_factors_studies
Límite:
Adult
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Child
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Female
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Humans
Idioma:
En
Revista:
Am J Med Genet A
Asunto de la revista:
GENETICA MEDICA
Año:
2016
Tipo del documento:
Article
País de afiliación:
Francia