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Practical Recommendations for Diagnosis and Management of Respiratory Muscle Weakness in Late-Onset Pompe Disease.
Boentert, Matthias; Prigent, Hélène; Várdi, Katalin; Jones, Harrison N; Mellies, Uwe; Simonds, Anita K; Wenninger, Stephan; Barrot Cortés, Emilia; Confalonieri, Marco.
Afiliación
  • Boentert M; Department of Sleep Medicine and Neuromuscular Disorders, Münster University Hospital, Münster 48149, Germany. matthias.boentert@ukmuenster.de.
  • Prigent H; Physiology Department and Neuromuscular Home Ventilation Unit, Raymond Poincaré University Hospital, Garches 92380, France. helene.prigent@aphp.fr.
  • Várdi K; Respiratory Rehabilitation and Sleep Center, Törökbálint Chest Hospital, Törökbálint 2045, Hungary. katalinvardi@gmail.com.
  • Jones HN; Department of Surgery, Duke University, Division of Speech Pathology & Audiology, Durham, NC 27710, USA. harrison.jones@duke.edu.
  • Mellies U; Department of Pediatric Pulmonology and Sleep Medicine, University of Duisburg-Essen, Children's Hospital, Essen 45147, Germany. uwe.mellies@uk-essen.de.
  • Simonds AK; Academic and Clinical Department of Sleep and Breathing, Royal Brompton & Harefield NHS Foundation Trust, London SW3 6NP, UK. a.simonds@rbht.nhs.uk.
  • Wenninger S; Friedrich-Baur-Institute, Department of Neurology, Ludwig-Maximilians-University, Munich 80336, Germany. stephan.wenninger@med.uni-muenchen.de.
  • Barrot Cortés E; Medical-Surgical Unit of Respiratory Diseases, University Hospital Virgen del Rocio, Seville 41013, Spain. emilia.barrot.sspa@juntadeandalucia.es.
  • Confalonieri M; Department of Pulmonology, University Hospital of Cattinara, Trieste 34149, Italy. marco.confalonieri@aots.sanita.fvg.it.
Int J Mol Sci ; 17(10)2016 Oct 17.
Article en En | MEDLINE | ID: mdl-27763517

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Insuficiencia Respiratoria / Músculos Respiratorios / Enfermedad del Almacenamiento de Glucógeno Tipo II / Debilidad Muscular Tipo de estudio: Diagnostic_studies / Guideline Límite: Adult / Humans / Infant Idioma: En Revista: Int J Mol Sci Año: 2016 Tipo del documento: Article País de afiliación: Alemania

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Insuficiencia Respiratoria / Músculos Respiratorios / Enfermedad del Almacenamiento de Glucógeno Tipo II / Debilidad Muscular Tipo de estudio: Diagnostic_studies / Guideline Límite: Adult / Humans / Infant Idioma: En Revista: Int J Mol Sci Año: 2016 Tipo del documento: Article País de afiliación: Alemania