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Lipofibromatosis-Like Neural Tumor: A Case Report and Review of the Literature.
Crumbach, Laura; Descotes, Françoise; Bringuier, Pierre-Paul; Poulalhon, Nicolas; Balme, Brigitte; Juliet, Tantot; Lopez, Jonathan; Harou, Olivier.
Afiliación
  • Crumbach L; Hospices Civils de Lyon, Hôpital Lyon Sud, Service d'anatomie et de cytologie pathologiques, Pierre Bénite, France.
  • Descotes F; Hospices Civils de Lyon, Hôpital Lyon Sud, Service de biochimie et de biologie moléculaire, Pierre Bénite, France.
  • Bringuier PP; Hospices Civils de Lyon, Groupement hospitalier Est, Service de biologie moléculaire, Bron, France.
  • Poulalhon N; Hospices Civils de Lyon, Hôpital Lyon Sud, Service de dermatologie, Pierre Bénite, France; and.
  • Balme B; Hospices Civils de Lyon, Hôpital Lyon Sud, Service d'anatomie et de cytologie pathologiques, Pierre Bénite, France.
  • Juliet T; Hospices Civils de Lyon, Hôpital Lyon Sud, Service d'anatomie et de cytologie pathologiques, Pierre Bénite, France.
  • Lopez J; Hospices Civils de Lyon, Hôpital Lyon Sud, Service de biochimie et de biologie moléculaire, Pierre Bénite, France.
  • Harou O; Cancer Research Center of Lyon, INSERM1052, CNRS5286, Université de Lyon, Lyon, France.
Am J Dermatopathol ; 42(11): 881-884, 2020 Nov.
Article en En | MEDLINE | ID: mdl-32618702
ABSTRACT
Lipofibromatosis-like neural tumors (LPF-NT) are soft tissue tumors characterized by a lipofibromatosis-like pattern, CD34/PS100 positivity, and recurrent NTRK1 gene rearrangement. It occurs mainly in pediatric patients or young adults. We report here, the first case of LPF-NT in a middle-aged adult initially misdiagnosed as a myoepithelial tumor. LPF-NT may have a locally aggressive course but no recurrence was seen after complete surgeries, whereas metastatic diseases remain exceptional.
Asunto(s)

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Neoplasias de los Tejidos Blandos Límite: Humans / Male / Middle aged Idioma: En Revista: Am J Dermatopathol Año: 2020 Tipo del documento: Article País de afiliación: Francia

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Neoplasias de los Tejidos Blandos Límite: Humans / Male / Middle aged Idioma: En Revista: Am J Dermatopathol Año: 2020 Tipo del documento: Article País de afiliación: Francia