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Lipid alterations in human frontal cortex in ALS-FTLD-TDP43 proteinopathy spectrum are partly related to peroxisome impairment.
Andrés-Benito, Pol; Gelpi, Ellen; Jové, Mariona; Mota-Martorell, Natalia; Obis, Èlia; Portero-Otin, Manuel; Povedano, Mònica; Pujol, Aurora; Pamplona, Reinald; Ferrer, Isidro.
Afiliación
  • Andrés-Benito P; Neuropathology, Bellvitge University Hospital-Bellvitge Biomedical Research Institute (IDIBELL, Hospitalet de Llobregat, Barcelona, Spain.
  • Gelpi E; Department of Pathology and Experimental Therapeutics, University of Barcelona, Barcelona, Spain.
  • Jové M; CIBERNED (Network Centre of Biomedical Research of Neurodegenerative Diseases, Institute of Health Carlos III, Ministry of Economy and Competitiveness, Madrid, Spain.
  • Mota-Martorell N; International Initiative for Treatment and Research Initiative to Cure ALS (TRICALS, Utrecht, The Netherlands.
  • Obis È; Neurological Tissue Bank of the Biobanc-Hospital Clínic-Institut d'Investigacions Biomèdiques August Pi I Sunyer (IDIBAPS, Barcelona, Spain.
  • Portero-Otin M; Institute of Neurology, Medical University of Vienna, Vienna, Austria.
  • Povedano M; Department of Experimental Medicine, University of Lleida - Lleida Biomedical Research Institute (UdL-IRBLleida, Lleida, Spain.
  • Pujol A; Department of Experimental Medicine, University of Lleida - Lleida Biomedical Research Institute (UdL-IRBLleida, Lleida, Spain.
  • Pamplona R; Department of Experimental Medicine, University of Lleida - Lleida Biomedical Research Institute (UdL-IRBLleida, Lleida, Spain.
  • Ferrer I; Department of Experimental Medicine, University of Lleida - Lleida Biomedical Research Institute (UdL-IRBLleida, Lleida, Spain.
Neuropathol Appl Neurobiol ; 47(4): 544-563, 2021 06.
Article en En | MEDLINE | ID: mdl-33332650

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Peroxisomas / Metabolismo de los Lípidos / Proteinopatías TDP-43 / Lóbulo Frontal / Esclerosis Amiotrófica Lateral Límite: Aged / Aged80 / Female / Humans / Male / Middle aged Idioma: En Revista: Neuropathol Appl Neurobiol Año: 2021 Tipo del documento: Article País de afiliación: España

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Peroxisomas / Metabolismo de los Lípidos / Proteinopatías TDP-43 / Lóbulo Frontal / Esclerosis Amiotrófica Lateral Límite: Aged / Aged80 / Female / Humans / Male / Middle aged Idioma: En Revista: Neuropathol Appl Neurobiol Año: 2021 Tipo del documento: Article País de afiliación: España