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Epidemiology and geographic clustering of Erdheim-Chester disease in Italy and France.
Peyronel, Francesco; Haroche, Julien; Campochiaro, Corrado; Pegoraro, Francesco; Amoura, Zahir; Tomelleri, Alessandro; Mazzariol, Martina; Papo, Matthias; Cavalli, Giulio; Benigno, Giuseppe D; Fenaroli, Paride; Grigoratos, Chrysanthos; Mengoli, Maria C; Bonometti, Arturo; Berti, Emilio; Savino, Gustavo; Cives, Mauro; Neri, Iria; Pacinella, Gaetano; Tuttolomondo, Antonino; Marano, Massimo; Muratore, Francesco; Manfredi, Andreina; Broccoli, Alessandro; Zinzani, Pier L; Didona, Biagio; Massaccesi, Chiara; Buono, Andrea; Ammirati, Enrico; Di Lernia, Vito; Dagna, Lorenzo; Vaglio, Augusto; Cohen-Aubart, Fleur.
Afiliación
  • Peyronel F; Nephrology and Dialysis Unit, Azienda Ospedaliera Universitaria Meyer IRCCS, Florence, Italy.
  • Haroche J; Department of Experimental and Clinical Medicine, University of Florence, Florence, Italy.
  • Campochiaro C; Sorbonne University, Assistance Publique-Hôpitaux de Paris, Pitié-Salpêtrière Hospital, Internal Medicine Department 2, French National Referral Center for Rare Systemic Diseases and Histiocytoses, Centre d'immunologie et des maladies infectieuses (Cimi INSERM Unité Mixte de Recherche Scientifique-1
  • Pegoraro F; Unit of Immunology, Rheumatology, Allergy and Rare Diseases, Istituto di Ricovero e Cura a Carattere Scientifico San Raffaele Scientific Institute, Milan, Italy.
  • Amoura Z; Vita-Salute San Raffaele University, Milan, Italy.
  • Tomelleri A; Department of Health Science, University of Florence, Florence, Italy.
  • Mazzariol M; Sorbonne University, Assistance Publique-Hôpitaux de Paris, Pitié-Salpêtrière Hospital, Internal Medicine Department 2, French National Referral Center for Rare Systemic Diseases and Histiocytoses, Centre d'immunologie et des maladies infectieuses (Cimi INSERM Unité Mixte de Recherche Scientifique-1
  • Papo M; Unit of Immunology, Rheumatology, Allergy and Rare Diseases, Istituto di Ricovero e Cura a Carattere Scientifico San Raffaele Scientific Institute, Milan, Italy.
  • Cavalli G; Vita-Salute San Raffaele University, Milan, Italy.
  • Benigno GD; Department of Medical Sciences, University of Turin, Turin, Italy.
  • Fenaroli P; Sorbonne University, Assistance Publique-Hôpitaux de Paris, Pitié-Salpêtrière Hospital, Internal Medicine Department 2, French National Referral Center for Rare Systemic Diseases and Histiocytoses, Centre d'immunologie et des maladies infectieuses (Cimi INSERM Unité Mixte de Recherche Scientifique-1
  • Grigoratos C; Unit of Immunology, Rheumatology, Allergy and Rare Diseases, Istituto di Ricovero e Cura a Carattere Scientifico San Raffaele Scientific Institute, Milan, Italy.
  • Mengoli MC; Renal Unit, Parma University Hospital, Parma, Italy.
  • Bonometti A; Nephrology and Dialysis Unit, Azienda Unità Sanitaria Locale-Istituto di Ricovero e Cura a Carattere Scientifico Reggio Emilia, Reggio Emilia, Italy.
  • Berti E; Cardiology Division, Fondazione Toscana Gabriele Monasterio, Pisa, Italy.
  • Savino G; Operative Unit of Pathology, Azienda Unità Sanitaria Locale-Istituto di Ricovero e Cura a Carattere Scientifico Reggio Emilia, Reggio Emilia, Italy.
  • Cives M; Pathology Unit, Istituto di Ricovero e Cura a Carattere Scientifico Humanitas Clinical and Research Hospital, Rozzano, Italy.
  • Neri I; Department of Biomedical Sciences, Humanitas University, Pieve Emanuele, Italy.
  • Pacinella G; Dermatology Unit, Fondazione Istituto di Ricovero e Cura a Carattere Scientifico Ca' Granda Ospedale Maggiore Policlinico, Milan, Italy.
  • Tuttolomondo A; Ocular Oncology Unit, Fondazione Policlinico Universitario A. Gemelli Istituto di Ricovero e Cura a Carattere Scientifico, Rome, Italy.
  • Marano M; Università Cattolica del Sacro Cuore, UCSC, Rome, Italy.
  • Muratore F; Division of Medical Oncology, Azienda Ospedaliero-Universitaria Consorziale Policlinico di Bari, Bari, Italy.
  • Manfredi A; Department of Interdisciplinary Medicine, University of Bari "Aldo Moro," Bari, Italy.
  • Broccoli A; Dermatology Unit, Istituto di Ricovero e Cura a Carattere Scientifico Azienda Ospedaliero Universitaria di Bologna, Policlinico S. Orsola-Malpighi, Bologna, Italy.
  • Zinzani PL; Internal Medicine and Stroke Care Ward, Department of Promoting Health, Maternal-Infant, Excellence and Internal and Specialized Medicine G. D'Alessandro, University of Palermo, Palermo, Italy.
  • Didona B; Internal Medicine and Stroke Care Ward, Department of Promoting Health, Maternal-Infant, Excellence and Internal and Specialized Medicine G. D'Alessandro, University of Palermo, Palermo, Italy.
  • Massaccesi C; Unit of Neurology, Neurophysiology, Neurobiology and Psychiatry, Department of Medicine and Surgery, Università Campus Bio-Medico di Roma, Rome, Italy.
  • Buono A; Fondazione Policlinico Universitario Campus Bio-Medico, Rome, Italy.
  • Ammirati E; Rheumatology Unit, Azienda Unità Sanitaria Locale-Istituto di Ricovero e Cura a Carattere Scientifico di Reggio Emilia, University of Modena and Reggio Emilia, Reggio Emilia, Italy.
  • Di Lernia V; Rheumatology Unit, University of Modena and Reggio Emilia, Azienda Policlinico of Modena, Modena, Italy.
  • Dagna L; Istituto di Ricovero e Cura a Carattere Scientifico Azienda Ospedaliero-Universitaria di Bologna Istituto di Ematologia "Seràgnoli", Bologna, Italy.
  • Vaglio A; Dipartimento di Scienze Mediche e Chirurgiche, Università di Bologna, Bologna, Italy.
  • Cohen-Aubart F; Istituto di Ricovero e Cura a Carattere Scientifico Azienda Ospedaliero-Universitaria di Bologna Istituto di Ematologia "Seràgnoli", Bologna, Italy.
Blood ; 142(24): 2119-2123, 2023 12 14.
Article en En | MEDLINE | ID: mdl-37871575
ABSTRACT
This geoepidemiological study, performed in Italy and France, shows that Erdheim-Chester disease is increasingly diagnosed and cases cluster in specific geographic areas, namely southern Italy and central France. Disease frequency inversely correlates with the Human Development Index.
Asunto(s)

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Enfermedad de Erdheim-Chester Límite: Humans País/Región como asunto: Europa Idioma: En Revista: Blood Año: 2023 Tipo del documento: Article País de afiliación: Italia

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Enfermedad de Erdheim-Chester Límite: Humans País/Región como asunto: Europa Idioma: En Revista: Blood Año: 2023 Tipo del documento: Article País de afiliación: Italia