RESUMEN
Abstract Clinical data: Infant, 7 months, female, referred to our department at one month of age, suspecting of congenital heart disease for further investigation. Chest radiography: Demonstrates cardiomegaly and prominent pulmonary vascular markings. Electrocardiography: Shows right ventricular hypertrophy and left anterior fascicular block. Echocardiography: Evidenced common atrioventricular valve with two orifices and the left superior pulmonary vein draining on the brachiocephalic vein. Computed tomography angiography: This complementary imaging exam was performed to confirm the diagnosis. Diagnosis: The patient presented an association between AVSD and PAPVC, a rare combination. The clinical picture of heart failure was preponderant, characterized by need for diuretics and complementary exams findings, and early surgical treatment was indicated. Operation: The operation was performed through a median sternotomy with 123 minutes of cardiopulmonary bypass and 89 minutes of cross-clamping time. The patient had no postoperative complications, remaining 10 days hospitalized.
Asunto(s)
Humanos , Femenino , Lactante , Anomalías Múltiples/diagnóstico por imagen , Malformaciones Vasculares/diagnóstico por imagen , Cardiopatías Congénitas/diagnóstico por imagen , Defectos del Tabique Interatrial/diagnóstico por imagen , Venas Pulmonares/anomalías , Venas Pulmonares/cirugía , Anomalías Múltiples/cirugía , Puente Cardiopulmonar , Electrocardiografía , Malformaciones Vasculares/cirugía , Angiografía por Tomografía Computarizada , Cardiopatías Congénitas/cirugía , Defectos del Tabique Interatrial/cirugíaAsunto(s)
Humanos , Femenino , Lactante , Tetralogía de Fallot/complicaciones , Tetralogía de Fallot/diagnóstico por imagen , Síndrome de Bland White Garland/complicaciones , Síndrome de Bland White Garland/diagnóstico por imagen , Tetralogía de Fallot/cirugía , Ecocardiografía , Radiografía Torácica , Resultado del Tratamiento , Electrocardiografía , Síndrome de Bland White Garland/cirugía , Angiografía por Tomografía ComputarizadaRESUMEN
CLINICAL DATA: Infant, 7 months, female, referred to our department at one month of age, suspecting of congenital heart disease for further investigation. CHEST RADIOGRAPHY: Demonstrates cardiomegaly and prominent pulmonary vascular markings. ELECTROCARDIOGRAPHY: Shows right ventricular hypertrophy and left anterior fascicular block. ECHOCARDIOGRAPHY: Evidenced common atrioventricular valve with two orifices and the left superior pulmonary vein draining on the brachiocephalic vein. COMPUTED TOMOGRAPHY ANGIOGRAPHY: This complementary imaging exam was performed to confirm the diagnosis. DIAGNOSIS: The patient presented an association between AVSD and PAPVC, a rare combination. The clinical picture of heart failure was preponderant, characterized by need for diuretics and complementary exams findings, and early surgical treatment was indicated. OPERATION: The operation was performed through a median sternotomy with 123 minutes of cardiopulmonary bypass and 89 minutes of cross-clamping time. The patient had no postoperative complications, remaining 10 days hospitalized.