[Severe aortic stenosis in the neonate and infant under 6 months old]. / Estenosis aórtica severa en el recién nacido y lactante menor de seis meses.

24 patients with diagnosed aortic stenosis are reported. Clinical symptoms started before 6 months of age (between 24 hours and 6 months, average 87 days). In all cases aortic stenosis was the only existing malformation, except in one patient who had a small muscular ventricular septal defect and in another case who had a patent ductus arteriosus. Clinical symptoms were early and notable. In nineteen there was congestive heart failure whose appearance in the first week of like was a bad prognosis. Relationship between severity of aortic stenosis and electrocardiographic findings was closer than in older patients. Death rate was very high in children who had not been operated (5 out of 12). Of children who received surgery only one died out of 12. Treatment, therefore, in this pathology must be aggressive.

[Di Giorge's syndrome with congenital heart disease (author's transl)]. / Síndrome de Di Giorge Estudio cardiológico en tres casos.

Authors describe three cases of Di Giorge's syndrome (thymic and parathyroid aplasia) proved through anatomical study postmorten, associated with cardiac malformations (Tetralogy of Fallot with pulmonary atresia, persistent truncus arteriosus and large patent ductus arteriosus). Clinical characteristics of the stated syndrome are analized with special reference to congenital heart diseases that are included in it.

[Congenital heart block and pacemaker implantation (author's transl)]. / Bloqueo cardíaco congénito con implantación de marcapaso

A six years old boy was sent to our service due to a loss of conscience spell. He had no preceding history E.K.G. showed a complete A-V block. Laboratory findings were within normal limits. Cardiac catheterism was performed and it ruled out any antomic abnormality, making evident a good contraction ability. To decide pacemaker implantation we evaluted: 1. That cardiac frequency was not increased by exercise neither by action of pharmacologyc agents (atropine, insoproterenol).-2. The existence of wide and bizarre QRS ocmplex.-3. And dizziness spels. The patient has been controlled during the past two years. Parasistolia has appeared, not showing modification till today.

[Smith-Lemli-Opitz syndrome. Cardiologic considerations (author's transl)]. / Síndrome de Smith-Lemli-Opitz. Consideraciones cardiológicas

A new case of the Smith-Lemli-Opitz Syndrome is reported, associated with a type of congenital cardiopathy not described previously in this syndrome.