RESUMO
A 71-year-old woman presented with an acute, massive pulmonary embolism. As a Jehovah's Witness, she was not willing to accept thrombolysis because of the potential risk of bleeding requiring blood transfusion. The patient was successfully treated with catheter thrombectomy, using rheolytic and fragmentation devices. (CHEST 2000; 117:594-597)
Assuntos
Cateterismo de Swan-Ganz , Cristianismo , Embolia Pulmonar/terapia , Trombectomia , Idoso , Feminino , Humanos , Embolia Pulmonar/diagnóstico por imagem , Cintilografia , Terapia Trombolítica , Recusa do Paciente ao Tratamento , Relação Ventilação-Perfusão/fisiologiaAssuntos
Ponte de Artéria Coronária , Aneurisma Intracraniano/cirurgia , Infarto do Miocárdio/cirurgia , Escleroderma Sistêmico/complicações , Hemorragia Subaracnóidea/cirurgia , Feminino , Humanos , Aneurisma Intracraniano/complicações , Pessoa de Meia-Idade , Infarto do Miocárdio/complicações , Hemorragia Subaracnóidea/complicaçõesRESUMO
The Rothmund-Thomson syndrome is a rare autosomal recessive condition. It is primarily a clinical diagnosis with manifestations that include poikiloderma, short stature, sparse hair, juvenile cataracts, small hands and feet, bone defects, photosensitivity, hypogonadism, defective dentition, onychodystrophy, and hyperkeratosis. There is only one published case of associated gastrointestinal abnormalities. We report a patient with Rothmund-Thomson syndrome with annular pancreas and duodenal stenosis.