RESUMO
Three cases of diffuse esophageal leiomyomatosis are discussed. Two of these are familial one, the mother being affected. These familial cases can occur in association with Alport's syndrome. The occurrence of a case of esophageal leiomyomatosis imply a familial survey and the search of a renal or ocular disease. The surgical treatment of this affection in sub total oesophagectomy with esophageal substitution (with the colon especially). The long term prognosis is unknown, with the risk of renal failure if Alport's syndrome is associated or of other leiomyomatous localisation.
Assuntos
Neoplasias Esofágicas/patologia , Leiomioma/patologia , Criança , Pré-Escolar , Neoplasias Esofágicas/genética , Esofagite/etiologia , Feminino , Seguimentos , Refluxo Gastroesofágico/etiologia , Humanos , Hipertrofia , Leiomioma/genética , MasculinoRESUMO
Papillary carcinoma is rare as it represents only 5 p. cent of carcinomas of the common bile duct. The authors report 4 cases and emphasize the special characteristics of this carcinoma. The long prodromal phase, dominated by attacks of cholangitis and the incomplete appearance of the jaundice when fully constituted. It affects mainly the common bile duct and has, on microscopy, a villous appearance. Its papillary structure consists of fine coalescent fringes producing a typical glandular appearance. Finally, it evolves very little, therefore there is a good hope of survival even after palliative treatment.