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Pediatr Blood Cancer ; 67(11): e28679, 2020 11.
Artigo em Inglês | MEDLINE | ID: mdl-32860659

RESUMO

Composite sarcoma of bone is a very rare entity that primarily affects adolescent and young adult patients. It usually combines areas of liposarcoma and osteosarcoma, and up to 60% of cases have metastatic disease at diagnosis. It is a highly aggressive pathology with intrinsic resistance to bone sarcoma conventional treatments. The prognosis is poor, with long-term survival rates not exceeding 30%. We present the case of an adolescent female diagnosed with an aggressive composite sarcoma of bone with rhabdomyosarcoma foci and loco-regional lymph node involvement.


Assuntos
Neoplasias Ósseas/secundário , Osteossarcoma/secundário , Rabdomiossarcoma/patologia , Neoplasias de Tecidos Moles/secundário , Adolescente , Neoplasias Ósseas/cirurgia , Feminino , Humanos , Metástase Linfática , Osteossarcoma/cirurgia , Prognóstico , Rabdomiossarcoma/cirurgia , Neoplasias de Tecidos Moles/cirurgia
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