Hemangioma arteriovenoso (aneurismacirsoide) subungueal / Subungual arteriovenous tumour (cirsoid aneurysm)

El hemangioma arteriovenoso subungueal es una entidad infrecuente y de carácter benigno descripta como una proliferación de los canales de Sucquet-Hoyer del cuerpo glómico. Se describe un caso y se enfatiza en la importancia del conocimiento de sus diagnósticos diferenciales y se realiza una actualización del tema (AU)

The subungueal arteriovenous tumour is an rare benign entity and it has been described as a proliferation of Sucquet-Hoyer channels of the glomusbody. A case report is presented and we emphasizes in the differential diagnosis. An update is made (AU)

Mycosis fungoides presenting with extensive pyoderma gangrenosum-like ulcers.

Mycosis fungoides (MF) may present with atypical clinical manifestations. Usually it mimics various chronic dermatoses, with the appearance of ulcers during the tumour stage. Infrequently, cutaneous ulcers are the main or initial sign of lymphoma. We report the case of a man who presented multiple skin lesions that clinically appeared to be pyoderma gangrenosum (PG). However, histological and immunohistochemical examination revealed MF. This case illustrates that PG-like ulcers maybe atypical cutaneous manifestations of MF and exceptionally the presenting sign of this disease.

[Ulcerated cutaneous lymphoma. 10 years of experience]. / Linfomas cutáneos ulcerados. Diez años de experiencia.

Patients with lymphomas and cutaneous ulcers have a poor prognosis. Commonly the ulcers occur later in the course of lymphomas and may be the source of sepsis. From 59 patients with lymphoma and skin involvement, 12 patients who presented with ulcers were retrospectively analyzed between January 1990 to December 1999. More frequently ulcers were multiple, necrotic, infected and placed on tumors. Sepsis was the main cause of mortality in 10 patients and most cases were secondary to Staphylococcus aureus and Pseudomonas aeruginosa. Factors associated with poor prognosis were febrile neutropenia after chemotherapy and generalized involvement by the lymphoma. Mean survival of deceased patients after onset of ulcers was 6.27 months. We emphasize the importance of an appropriate microbiological study and a prompt therapy.

Linfomas cutáneos ulcerados. Diez años de experiencia. / [Ulcerated cutaneous lymphoma. 10 years of experience]

Patients with lymphomas and cutaneous ulcers have a poor prognosis. Commonly the ulcers occur later in the course of lymphomas and may be the source of sepsis. From 59 patients with lymphoma and skin involvement, 12 patients who presented with ulcers were retrospectively analyzed between January 1990 to December 1999. More frequently ulcers were multiple, necrotic, infected and placed on tumors. Sepsis was the main cause of mortality in 10 patients and most cases were secondary to Staphylococcus aureus and Pseudomonas aeruginosa. Factors associated with poor prognosis were febrile neutropenia after chemotherapy and generalized involvement by the lymphoma. Mean survival of deceased patients after onset of ulcers was 6.27 months. We emphasize the importance of an appropriate microbiological study and a prompt therapy.

Nodulo de sister Joseph como presentación del carcinoma de cuello uterino / Sister Josephs nodule how presentation of the uterine cervix carcinoma

Las metástasis umbilicares son infrecuentes y reciben el nombre de nódulo de Sistes Joseph. Presentamos una mujer de 51 años que consultó por autodetectarse dos formaciones tumorales subcutáneas, la primera de tres meses de evolución en el ombligo y la restante en la pared anterior del tórax. La biopsis de la lesión umbilical imformó carcinoma epidermoide queratinizante subcutáneo diagnosticándose la neoplasia primaria en el cuello uterino. En el presente trabajo se realiza una reviosión bibliográfica del nódulo de Sister Joseph. Destacamos su escasa frecuencia como manifestación inicial del carcinoma de cuello uterino debiéndose considerar en el diagnóstico diferencial de los tumores de ombligo(AU)

Nodulo de sister Joseph como presentación del carcinoma de cuello uterino / Sister Joseph's nodule how presentation of the uterine cervix carcinoma

Las metástasis umbilicares son infrecuentes y reciben el nombre de nódulo de Sistes Joseph. Presentamos una mujer de 51 años que consultó por autodetectarse dos formaciones tumorales subcutáneas, la primera de tres meses de evolución en el ombligo y la restante en la pared anterior del tórax. La biopsis de la lesión umbilical imformó carcinoma epidermoide queratinizante subcutáneo diagnosticándose la neoplasia primaria en el cuello uterino. En el presente trabajo se realiza una reviosión bibliográfica del nódulo de Sister Joseph. Destacamos su escasa frecuencia como manifestación inicial del carcinoma de cuello uterino debiéndose considerar en el diagnóstico diferencial de los tumores de ombligo

[Isolated neurofibroma of the common bile duct]. / Neurofibroma intraparietal aislado del colédoco.

The neurogenic tumors in the biliary tract are rare and usually are amputation neuroma that occur after cholecystectomy. We describe a case of isolated neurofibroma of the common bile duct in a young man not cholecystectomized. The patient suffered recurrent episodes of abdominal pain, vomiting and weight loss without clinical signs of Von Recklinghausen's disease or jaundice. The hepatogram was normal. The echography indicated a solid formation with obstruction of the proximal common bile duct. In the ERCP the stenosis was found. Surgical excision of the tumor and anastomosis of bilateral hepatic ducts and jejunum were carried out. At microscopic examination intraparietal neurofibroma of the common bile duct was found. As isolated entity, we know of only one reported case.

Neurofibroma intraparietal aislado del colédoco. / [Isolated neurofibroma of the common bile duct]

The neurogenic tumors in the biliary tract are rare and usually are amputation neuroma that occur after cholecystectomy. We describe a case of isolated neurofibroma of the common bile duct in a young man not cholecystectomized. The patient suffered recurrent episodes of abdominal pain, vomiting and weight loss without clinical signs of Von Recklinghausens disease or jaundice. The hepatogram was normal. The echography indicated a solid formation with obstruction of the proximal common bile duct. In the ERCP the stenosis was found. Surgical excision of the tumor and anastomosis of bilateral hepatic ducts and jejunum were carried out. At microscopic examination intraparietal neurofibroma of the common bile duct was found. As isolated entity, we know of only one reported case.