RESUMO
Spontaneous intestinal intramural haematomas are uncommon in the absence of trauma and may occur in those on anticoagulation. A young girl presented with generalised abdominal pain and was found to have pneumoperitoneum. She underwent an exploratory laparotomy and was found to have multiple ileal intramural haematomata with an area of possible perforation with a collection of pus. We believe that this is the first reported case of a rupture of spontaneous intestinal intramural haematoma in a young girl with no history of anticoagulation use or coagulation disorders.
Assuntos
Hematoma/cirurgia , Doenças do Íleo/cirurgia , Dor Abdominal/etiologia , Adolescente , Feminino , Hematoma/diagnóstico por imagem , Hematoma/patologia , Humanos , Doenças do Íleo/diagnóstico por imagem , Doenças do Íleo/patologia , Pneumoperitônio/etiologia , Pneumoperitônio/cirurgia , Ruptura Espontânea/etiologia , Ruptura Espontânea/cirurgia , Tomografia Computadorizada por Raios X , Vômito/etiologiaRESUMO
Inflammatory myofibroblastic tumours (IMTs) are rare tumours with unpredictable biological behaviour ranging from benign to locally invasive and rarely, distant metastasis. While neurofibromatosis type 1 (NF1) may manifest with gastrointestinal soft tissue tumours, this is the first report in the literature that describes an IMT occurring in a NF1 patient who presented with intestinal obstruction. Our patient presented with intestinal obstruction secondary to an obstructing terminal ileum mesenteric tumour. En bloc bowel resection was performed, with histology revealing an IMT and an adjacent neurofibroma. The resection margins were clear and the patient was free of recurrence at six months.
