RESUMO
Myositis ossificans progressiva is an unusual autosomal-dominant inherited disease characterized by congenital malformations and osseous metaplasia of the fascia of the muscles and connective tissue leading to ossification of the relevant area. The case report is remarkable in that eight members of the same family over five generations manifested the exclusive localization of the disease in the maxillofacial region.
Assuntos
Miosite Ossificante/genética , Músculos Pterigoides/patologia , Adulto , Tecido Conjuntivo/patologia , Progressão da Doença , Fáscia/patologia , Feminino , Genes Dominantes , Humanos , Músculo Masseter/patologia , Miosite Ossificante/patologia , Miosite Ossificante/fisiopatologia , Ossificação Heterotópica/patologia , Linhagem , Músculos Pterigoides/fisiopatologia , Músculo Temporal/patologiaRESUMO
Actually, oral medicine and maxillo-facial surgery are really moving. There is no detail's study of the different aspects of our specialty, so we had like to realise a "picture" of our activity in the private sector in 1993. In this evaluation, an answering has been sent to the whole professional. Per 37.2% of answers have been received. The aim of this article is describing you the oral medicine and maxillo-facial surgery population following, in 4 points: old and sex demography; university and post-university formation; surgical or no activity repartition; exercises and installations.