RESUMO
Pulmonary valvotomy combined with a central shunt ("U shaped" Gore-tex graft) for palliative treatment of critical pulmonary stenosis is reported. The same graft was employed for right ventricular outflow reconstruction at the time of the definitive repair.
Assuntos
Cuidados Paliativos/métodos , Estenose da Valva Pulmonar/cirurgia , Valva Pulmonar/cirurgia , Aorta/cirurgia , Prótese Vascular , Humanos , Recém-Nascido , Masculino , Artéria Pulmonar/cirurgiaRESUMO
Anomalous origin of one pulmonary artery from the ascending aorta without associated intracardiac defects is a rare congenital malformation. About 60 anatomic and surgical descriptions have been reported in the literature. Up to 1974, 22 of the 50 reported cases underwent surgical correction with a 40% mortality rate. The natural history without surgery is poor with a very high mortality during the first year of life. Successful anatomic correction of anomalous origin of right pulmonary artery from the ascending aorta in a 6 months old female is reported.