[Ehlers-Danlos's syndrome type II. A family study]. / Síndrome de Ehlers-Danlos tipo II. Estudio familiar.

We describe the presence of EDS type II in a family whose diagnosis was lately established by medical consultation of one of its members suffering from hyperuricemia and gout. We stress the relevance of an early diagnosis of this syndrome as a means to prevent and reduce as much as possible cardiovascular, hemorrhagic and surgical systemic complications associated to this disease.

Temporal arteritis in a northwestern area of Spain: study of 57 biopsy proven patients.

Fifty-seven patients, diagnosed with temporal arteritis by biopsy from 1981 to 1990, were studied. The average annual incidence rate/100,000 population aged 50 and older, which was slightly lower than those from other Mediterranean countries of Europe, was 6. Apart from a predominance of males, age, clinical and laboratory features were similar to those reported from other parts of the world. All patients received corticosteroid therapy, the majority of them recovered completely. Fifty-four were followed; 34 had already finished treatment (mean: 22 months, range: 12-50). Relapses occurred more commonly after 12 months of therapy, when the amount of prednisone given was low or discontinued.

[Lupus myopathy refractory to steroid treatment]. / Miopatía lúpica refractaria al tratamiento esteroideo.

A 58-year-old patient with lupus erythematosus (LE) who needed treatment with azathioprine, due to resistant myopathy to steroids, is presented. Clinical and histological features, as well as therapy, are discussed.