1.
Clin Exp Immunol
; 202(3): 379-383, 2020 12.
Artigo
em Inglês
| MEDLINE
| ID: mdl-32640035
RESUMO
Primary pneumococcal peritonitis is a rare infection that has been described in women but has not been previously linked with immunodeficiency. The complement system plays a central role in immune defence against Streptococcus pneumoniae and, in order to evade complement attack, pneumococci have evolved a large number of mechanisms that limit complement-mediated opsonization and subsequent phagocytosis. We investigated an apparently immunocompetent woman with primary pneumococcal peritonitis and identified a family with deficiency for complement factor I. Primary pneumococcal peritonitis should be considered a possible primary immunodeficiency presentation.
Assuntos
Complemento C3/deficiência , Doenças da Deficiência Hereditária de Complemento/imunologia , Peritonite/imunologia , Infecções Pneumocócicas/imunologia , Streptococcus pneumoniae/imunologia , Adolescente , Complemento C3/imunologia , Feminino , Doenças da Deficiência Hereditária de Complemento/patologia , Humanos , Peritonite/patologia , Infecções Pneumocócicas/patologia
2.
Artigo
em Inglês
| WHO IRIS
| ID: who-170273