[Dilated vestibular aqueduct syndrome in children. Report of a case]. / Síndrome del acueducto vestibular dilatado en la infancia. A propósito de un caso.

Enlarged vestibular aqueduct syndrome is a clinical condition characterized for a progressive perceptive deafness linked to a broadening of vestibular aqueduct greater than 1.5 mm without other otic abnormal structures. We report the case of a 2-year-old child with such congenital malformation. We have reviewed the actual literature and point out its clinical and physiopathologic features as well treatment possibilities of these cases.

Dacriocistorrinostomía externa con mitomicina C. Valoración clínica y anatómica mediante tomografía computarizada helicoidal / External dacryocystorhinostomy with mitomycin C. Clinical and anatomical evaluation with helical computed tomography

Objetivo: Evaluar el efecto de la aplicación intraoperatoria de mitomicina C (MMC) en la dacriocistorrinostomía (DCR) externa, sobre la evolución clínica y el tamaño de la osteotomía mediante tomografía computarizada helicoidal (TCH). Métodos: Se practicaron 17 DCR en 17 pacientes clasificados en dos grupos: grupo 1 o control (DCR sin MMC): 8 pacientes, y grupo 2 (DCR con MMC): 9 pacientes. La MMC intraoperatoria (0,2 mg/ml/2 minutos) se aplicó mediante hemosteta sobre la osteotomía. Los estudios con TCH se practicaron a las 24 horas, 1, 3 y 6 meses. Se valoró el grado de epífora y permeabilidad lagrimal. El cálculo del área de osteotomía fue obtenido mediante reconstrucción informatizada tridimensional y multiplanar de las TCH. Resultados: El seguimiento medio fue 10,47ñ4,1 meses (rango= 6-18 meses). La DCR con MMC resolvió la epífora en el 100 por ciento de los pacientes, versus 75 por ciento en el grupo control. En el grupo 2 el porcentaje de osteotomía permeable a los 6 meses, en comparación con el área de osteotomía inmediatamente tras la cirugía, fue 93,82ñ4,55 por ciento, frente al 64,81ñ9,68 por ciento en el grupo 1 (p<0,001). Existieron diferencias significativas desde el 1.er mes. Conclusiones: La MMC incrementa la tasa de éxitos de la DCR y reduce el cierre del área de la osteotomía (AU)

No disponible

[External dacryocystorhinostomy with mitomycin C. Clinical and anatomical evaluation with helical computed tomography]. / Dacriocistorrinostomía externa con mitomicina C. Valoración clínica y anatómica mediante tomografía computarizada helicoidal.

PURPOSE: To study the effect of intraoperative mitomycin C (MMC) in external dacryocystorhinostomy (DCR), on the clinical evolution and osteotomy size with helical computed tomography (HCT). METHODS: A total of 17 patients who had undergone DCR were randomly assigned to either a control group (8 patients) or an MMC group (9 patients). Intraoperative MMC (0.2 mg/ml/2 minutes) was applied to the osteotomy site. HCT scans were performed within 24 hours after surgery and then at 1, 3 and 6 months. The epiphora grade and lacrimal drainage system irrigation were evaluated after surgery. A computer-aided three-dimensional and multiplanar reconstruction was used to calculate the surface area of the osteotomy site. RESULTS: The mean follow-up was 10.47+/-4.1 months (range= 6-18 months). All patients (100%) remain asymptomatic in the MMC group and 5 patients (75%) in the control group. In the MMC group the percentage of the remaining osteotomy size in comparision with the osteotomy size immediately after surgery at the end of the sixth postoperative month was 93.82+/-4.55%, whereas that of the control group was only 64.81+/-9.68% (p<0,001). Statistically significant differences were noted at 1, 3 and 6 months. CONCLUSIONS: Intraoperative MMC may increase the success rates over the traditional DCR procedure and is effective in reducing the closure rate of the osteotomy after DCR.

[Retroperitoneal tumor arising from neural crest: ganglioneuroma+]. / Tumor retroperitoneal derivado de la cresta neural: ganglioneroma.

OBJECTIVES: This study shows the contribution of the different imaging methods in the diagnosis of retroperitoneal ganglineuroma. METHODS: A retroperitoneal mass was incidentally detected in a young male patient. Patient evaluation included plain abdominal radiography, intravenous urography, ultrasound and computed tomography. RESULTS: Ultrasound and computed tomography provide information on tumor characteristics and extent, although it has no diagnostic specifity and does not permit distinguishing ganglioneuroma from other neural crest tumors.