RESUMO
Myocardial bridging is a controversial topic that remained with no well-defined management protocol. We present a ten-year-old child with Noonan syndrome and a myocardial bridge.
Assuntos
Cardiomiopatia Hipertrófica , Ponte Miocárdica , Síndrome de Noonan , Cardiomiopatia Hipertrófica/complicações , Cardiomiopatia Hipertrófica/diagnóstico por imagem , Cardiomiopatia Hipertrófica/cirurgia , Criança , Ponte de Artéria Coronária , Humanos , Miocárdio , Síndrome de Noonan/complicações , Síndrome de Noonan/diagnóstico por imagem , Síndrome de Noonan/cirurgiaRESUMO
Anomalous aortic origin of the pulmonary artery is rare. It can affect either of the main branches and can be an important cause of neonatal respiratory distress. Early diagnosis and surgical repair is associated with improved survival and long-term outcomes.
Assuntos
Aorta/anormalidades , Doenças da Aorta/etiologia , Artéria Pulmonar/anormalidades , Trombose/etiologia , Aorta/diagnóstico por imagem , Aorta/cirurgia , Doenças da Aorta/diagnóstico , Doenças da Aorta/cirurgia , Humanos , Imageamento Tridimensional , Recém-Nascido , Masculino , Artéria Pulmonar/diagnóstico por imagem , Artéria Pulmonar/cirurgia , Trombose/diagnóstico , Trombose/cirurgia , Tomografia Computadorizada por Raios X , Procedimentos Cirúrgicos Vasculares/métodosRESUMO
Introduction. Pericardial effusion (PCE) and tamponade can cause significant morbidity and mortality in neonates. Such cases have been reported in the literature in various contexts. Case Presentation. A 6-day old neonate with meconium aspiration syndrome and persistent pulmonary hypertension of newborn on high frequency oscillator ventilation and inhaled nitric oxide was referred to our hospital with a large pericardial effusion causing hemodynamic compromise. Prompt pericardiocentesis led to significant improvement in the cardio-respiratory status and removal of the central line prevented the fluid from reaccumulating. Cellular and biochemical analysis aided in the diagnosis of catheter related etiology with possibility of infusate diffusion into the pericardial space. Conclusion. We present this paper to emphasize the importance of recognizing this uncommon but serious complication of central venous catheters in intensive care units. We also discuss the proposed hypothesis for the mechanism of production of PCE.