RESUMO
BACKGROUND: Primary broad ligament leiomyosarcoma (LMS) is an extremely rare tumor with few well-documented cases. We are aware of 15 previously reported observations. AIM: Report of a new case. CASE: In this report we report a case of a right pelvic sidewall leiomyosarcoma with involvement of the appendix in a 49-year-old woman. A hysterectomy, bilateral salpingo-oophorectomy, omentectomy and appendicectomy were done, without complications. The patient died five months later. The case illustrates the difficulty of correct diagnosis before intervention. On this occasion, review of the literature confirms that this site remains unusual and the management is difficult.
Assuntos
Ligamento Largo/patologia , Leiomiossarcoma/patologia , Neoplasias Uterinas/patologia , Apendicectomia , Neoplasias do Apêndice/patologia , Neoplasias do Apêndice/cirurgia , Ligamento Largo/cirurgia , Feminino , Humanos , Histerectomia , Leiomiossarcoma/cirurgia , Pessoa de Meia-Idade , Neoplasias Uterinas/cirurgiaRESUMO
BACKGROUND: The vast majority of primary vaginal cancers are squamous cell carcinoma. The leiomyosarcoma of the vagina is extremely rare neoplasm. It comprising 2% to 3% of vaginal malignancies. Only 77 cases have been reported up to date in Anglo-Saxon literature . AIM: Report of a new case CASE: We report a case of a patient 43 years old, single and presented a tumor of 7 cm to the detriment of the posterior wall of the vagina. The treatment consisted of a radical colpohysterectomy followed by postoperative radiotherapy. After 40 months, she is still alive without local or distant recurrence. CONCLUSION: This is a rare observation. The surgery is the basic treatment, the poor prognosis of these tumors remains linked especially to the histological grade.
Assuntos
Leiomiossarcoma , Neoplasias Vaginais , Adulto , Biópsia , Feminino , Seguimentos , Humanos , Histerectomia , Leiomiossarcoma/patologia , Leiomiossarcoma/radioterapia , Leiomiossarcoma/cirurgia , Cuidados Pós-Operatórios , Prognóstico , Dosagem Radioterapêutica , Radioterapia Adjuvante , Fatores de Tempo , Vagina/patologia , Neoplasias Vaginais/patologia , Neoplasias Vaginais/radioterapia , Neoplasias Vaginais/cirurgiaRESUMO
Prune Belly syndrome is characterized by a combination of megacystis, anterior abdominal wall distension with deficiency of the abdominal wall musculature, and bilateral cryptorchidism. Diagnosis is easy after 15 weeks of gestation, but may be difficult at the end of the first term. Authors report 2 cases of Prune Belly syndrome diagnosed at 11 and 14 weeks of gestation respectively. After literature review, diagnosis and prognosis particularities of this syndrome are discussed.
