RESUMO
Young-onset cerebellar syndromes are quite interesting and challenging for treating clinicians. While dealing with such cases, a clinician should be aware of rare possible causes too. We report a rare case of Gordon Holmes syndrome-an autosomal recessive cerebellar ataxia with endocrinal abnormalities.
Assuntos
Ataxia Cerebelar/diagnóstico , Hormônios Esteroides Gonadais/uso terapêutico , Hormônio Liberador de Gonadotropina/deficiência , Hipogonadismo/diagnóstico , Doenças Raras , Adulto , Ataxia Cerebelar/tratamento farmacológico , Ataxia Cerebelar/fisiopatologia , Humanos , Hipogonadismo/tratamento farmacológico , Hipogonadismo/fisiopatologia , Masculino , Exame Físico , Doenças Raras/diagnóstico , Doenças Raras/tratamento farmacológico , Doenças Raras/fisiopatologia , Resultado do TratamentoRESUMO
Dengue infection is gradually disseminating throughout the world in alarming proportions. It is a arbovirus infection,transmitted by aedes mosquitoes. It is a multi-systemic disorder associated with varied neurological complications. There is increased trend of development of neurological complications in dengue fever. The neurological complications arising due to dengue infection can be categorized into central and neuromuscular complications. The central nervous system disorders reported with dengue fever are encephalopathy,encephalitis and myelitis.Here we report a case of rhombencephalitis associated with dengue fever. The literature does not mention rhombencephalitis occurring with dengue illness.