RESUMO
BACKGROUND: Non-compaction of the left ventricular myocardium is an important cause of cardiomyopathy. There is no clear consensus about its diagnostic criteria or the diagnostic test of choice. MRI is increasingly used in the pediatric cardiac field because of its superior and objective image quality. OBJECTIVE: To compare the echocardiographic and MRI findings in four patients with recently diagnosed ventricular non-compaction. MATERIALS AND METHODS: We compared the extent of myocardial involvement shown at MRI and echocardiography in four individuals, two patients with echocardiographic diagnosis of left ventricular non-compaction, and two family members of one of the patients. RESULTS: In all patients, MRI showed wider area of involvement than echocardiography. A definite diagnosis was entertained in only two patients by echocardiography but in all by MRI. Cine imaging was diagnostic of the disease in all patients. Black-blood pool imaging with double-inversion recovery sequence also helped to visualize the abnormal areas by showing slow flow artifacts in the four- and two-chamber images. CONCLUSION: MRI provided better delineation of the extent of the abnormal trabeculation in patients with non-compaction of the left ventricular myocardium. It was particularly useful when the myocardial involvement was subtle, as in the asymptomatic family members.
Assuntos
Cardiomiopatia Hipertrófica/congênito , Cardiomiopatia Hipertrófica/diagnóstico , Ecocardiografia/métodos , Ventrículos do Coração/anormalidades , Imageamento por Ressonância Magnética/métodos , Disfunção Ventricular Esquerda/congênito , Disfunção Ventricular Esquerda/diagnóstico , Adolescente , Criança , Pré-Escolar , Feminino , Ventrículos do Coração/diagnóstico por imagem , Ventrículos do Coração/patologia , Humanos , Masculino , Projetos Piloto , Reprodutibilidade dos Testes , Sensibilidade e Especificidade , Índice de Gravidade de DoençaRESUMO
Isolation of a branch pulmonary artery from ductal closure is an unusual finding in patients with tetralogy of Fallot. A case report of a newborn is presented where the closing arterial duct was balloon-dilated and stented to reestablish blood supply to the affected lung as a strategy of improving systemic saturations and promoting the growth of the hiliar branch pulmonary artery. Five months after the initial palliation, complete surgical repair with stent removal was successfully achieved.
