RESUMO
Epithelioid hemangioendothelioma is a rare, low-grade malignant vascular tumour. It is frequently seen in the liver, but can occur in the lungs, bones, and other soft tissues. Although survival time might be reasonable in cases that can undergo liver transplantation, there is no consensus on the treatment of metastatic patients. We report a 24-year-old female patient with rapidly progressing malignant epithelioid hemangioendothelioma that presented with acute abdominal distension. The patient was refractory to anthracycline and Interferon treatment and died 6.5 months after the diagnosis.
Assuntos
Hemangioendotelioma Epitelioide/diagnóstico , Neoplasias Hepáticas/diagnóstico , Antígenos CD34/metabolismo , Antineoplásicos/uso terapêutico , Progressão da Doença , Evolução Fatal , Feminino , Hemangioendotelioma Epitelioide/tratamento farmacológico , Humanos , Imuno-Histoquímica , Interferons/uso terapêutico , Gordura Intra-Abdominal/metabolismo , Gordura Intra-Abdominal/patologia , Neoplasias Hepáticas/tratamento farmacológico , Molécula-1 de Adesão Celular Endotelial a Plaquetas/metabolismo , Tomografia Computadorizada por Raios X , Adulto JovemRESUMO
Renal cell carcinoma (RCC) has a high metastatic potential due to its hematogen and vascular features. It metastasizes frequently to the lungs, the bones, the liver, the lymph nodes and the brain. Metastasis of RCC to the head and neck region is quite rare. In this case report, two RCC patients with head and neck metastases are presented: one occurring after 5 years and the other occurring 17 years after diagnosis.
