RESUMO
Nephroblastoma, or Wilms tumor, is the most common renal neoplasm in children and accounts for approximately a fifth of all malignant growths in this age group. However, the incidence of Wilms tumor in adults is much less common, with less than 200 cases having been reported in the literature. In addition, since there are at least 53 synonyms for this tumor an adequate computer search for articles relating to this subject is difficult. Because of the scarcity of this disease in adults definite treatment modalities have not been accepted thoroughly until recently. The rationale for the present treatment modalities is based largely on the National Wilms Tumor Study groups 1 to 3. We present radiologic and histologic findings of this tumor in 2 additional cases. The current treatment modalities, consisting of chemotherapy with or without adjunctive radiotherapy, are discussed.
Assuntos
Neoplasias Renais/epidemiologia , Tumor de Wilms/epidemiologia , Adulto , Protocolos de Quimioterapia Combinada Antineoplásica/uso terapêutico , Terapia Combinada , Feminino , Humanos , Neoplasias Renais/diagnóstico , Neoplasias Renais/terapia , Pessoa de Meia-Idade , Nefrectomia , Prognóstico , Tumor de Wilms/diagnóstico , Tumor de Wilms/terapiaRESUMO
A large, multilocular cystic mass from the kidney of a 26-year-old woman was examined by light microscopy and transmission electron microscopy. Ultrastructurally the cysts were shown to be lined by smooth muscle cells, giving evidence that the cysts originated in smooth muscle. Thus the tumor is considered to be a multilocular cystic leiomyoma, an apparently unique renal tumor.
