IgG4-Related Disease (IgG4-RD) Presenting as a Mass in the Carotid Triangle Masquerading Paraganglioma.

IgG4-related disease (IgG4-RD) which is a protein disorder presented as a mass in the right carotid triangle in a 30 year male patient, who underwent battery of tests is described. The radiologist opined the mass as paraganglioma and the spindle shaped character of the mass also suggested neurogenic tumor in differential diagnosis. Reference to vascular surgeon also opined the same, and adviced for incisional biopsy. Histopathology report suggested IgG4-RD and immunochemistry confirmed the final diagnosis. The neck mass which we opined as a single organ disease, proved to be multiorgan disease in PET scan.

Tracheocele presenting with intermittent dysphonia: a case report.

We report a rare case of tracheocele presenting in an ENT setting. The referral was made on the basis of intermittent dysphonia. The aim of this report is to document the rare condition of tracheocele on the right side and to help raise the level of its awareness among the otolaryngologists. So far approximately thirty cases of this condition have been documented in the literature worldwide. An emphasis is placed on the mode of presentation and the management issues, as early diagnosis is crucial and offers a favorable prognosis. The right sided predilection of the swelling is due to anatomical reason and the cause of recurrent dysphonia is explained.

Glial Heterotopia in ENT-Two Case Reports and Review of Literature.

The purpose of presenting these case reports is to highlight the occurrence of heterotopic glial tissue of the tongue and nose in children. So far, literature review has revealed few case reports of such lesions in neonates, but our patients presented with this unique lesion at the age of two and a half years and 3 years. This is a rare congenital anomaly in the tongue, which can mimic a lingual thyroid, teratoma, dermoid cyst etc. Surgical excision is mandatory when the lesion causes obstructive symptoms. The authors discuss the problems in diagnosis, pathology and management and review the literature.

Extranodal manifestation of Rosai Dorfman Disease of the nasopharynx.

The aim of presenting this case is to highlight the fact that extranodal manifestation of Rosai Dorfman Disease (RDD) without lymphadenopathy was seen in a teenaged girl with recurrent episodes of epistaxis, due to a lobulated mass in the nasopharynx, which mimicked malignancy. This case is a rare presentation because the extranodal manifestation of RDD in multisystem organs are reported in literature, but the nasopharyngeal manifestation without lymphadenopathy is unique. The clinical presentation and surgical management of the case by endoscopic sinus surgery, the aetiopathology, differential diagnosis and review of literature are described here.

Pseudocyst of auricle - etiopathogenesis, treatement update and literature review.

Pseudocyst of the pinna, a benign idiopathic cystic swelling is an uncommon condition. In the medline search there are over 113 cases reported in literature. Engel in 1966 reported the incidence in Chinese community. In this review article we describe the etiopathogenesis, demographic statistics and treatment modalities.This is a retrospective study of six cases treated by the senior author in the dept of Otorhinolaryngology, Head & Neck Surgery, Apollo Hospital Chennai, South India between 1993 through 2003. There is preponderance of incidence in adult male (5 cases) and a single case in a female. The author highlights the modalities of treatment and opines that the surgical technique described by Lim et al, with little modification is the gold standard, which retains the architecture of the pinna. Conservative methods adopted by others have failed.

Oral submucous fibrosis-New dimensions in surgery.

The oral submucous fibrosis (OSMF) has been managed earlier by various medical and surgical modalities but none of these methods is found to give relief to these patients. Hence, a new method has been developed by us. Patients, who reported with pallor of the palate cheek, oropharyn and the tonsils, due to the fibrosis, leading on to mild, moderate to severe trismus, were given a good long-term rehef by this surgical method. This study involved 60 patients between 1979 and 2000 with a female-to-male ratio of 1∶3 with age ranging from 13 to 60 years suffering from the disease. The surgical method adopted in these cases used a single staged rotation tongue pedicle flap on either side from the dorsum of the tongue sutured to the raw area in the cheek without morbidity. In a 7-year follow up, we found the patients did not develop further fibrosis and the tongue flaps remained intact. The quality of life improved considerably and buccal mucosa is pink throughout the follow-up period. The modalities of treatment adopted are varied. Many tried the retro molar excision of the bands, which did not give long-term results. Others used excision of the whole fibrotic area with skin grafting, which also failed. Some have tried muscle pedicle flap from outside with postoperative morbidity and failure. Some surgeons have tried fat grafts in the cheek region (Yeh, Int J Oral Maxillo facial Surg 1996; 25; 130). The experience of the others who used versatile, vascular tongue flaps in the oral cavity after cancer clearance, prompted us to attempt this new technique in the present series with gratifying results. This is a break through in the surgical management of OSMF, where other treatment modalities failed.

Thyroplasty type I - Apollo hospital experience, with a brief review of literature.

Thyraphtsty Type I in Phonosurgery is one of the techniques first practised by Prof. Isshiki, a pioneer in this field. The technique that we adopted is a tittle different from his technique, which is highlighted in a series of six cases, done at Apollo Hospitals, Chennai from December 1997 to April 2001. The postoperative results were quite good and the patients could phonate without any effort Patients followed up for one year showed no deterioration in phonation and they are back in their profession. A brief review of literature is documented.

Office based trans nasal esophagoscopy, and its role.

Trans Nasal Esophagoscopy (TME) - a new concept to visualize the esophagus in office practice has obviated the conventional rigid esophagoscope, which is a cumbersome, time consuming procedure and sometimes associated with complications like perforation. Many surgeons in the West using flexible endoscope after air insufflation have tried this procedure. We fabricated a new gadget far the purpose of air insufflation in collaboration with the department of biomedical engineering, Apollo hospitals, Chennai which substitute oxygen insufflation through central supply or through the flow meter connected to an O(2) cylinder. In this article we have discussed various uses of the procedure in diagnosis A therapeutic application in an E.N.T office practice and also the unique technique of air insufflation with the new gadget.

Supraoesophageal manifestations of gerd- A myth or reality?

Gastroesophageal reflux disease (GERD) is a disease that has come to limelight in the rreent past to account for various ear, nose and throat disorders. Fifty patients from my outpatient department, presenting with chronic dry paroxysmal cough, choking spells, globus sensation, voice change, burning throat syndrome, dysphagia were evaluated, with both invasive and non-invasive techniques like Fibreoptic Nasoendoscopy, Nuclear Scintigraphy with technetium, Barium swallow, sans pH monitoring which is an expensive and laborious method.We have shown evidence of GER with help of Nasoendoscopy, which revealed posterior laryngitis, erythema of arytenoids and interarytenoid oedema. This is corroborated with Scintigraphy done in Nuclear Medicine department, which is our gold standard for labelling the cases as GERD. Basing on the investigations, we have treated successfully fifty cases with medical treatment consisting of H2 Hockers, proton pump inhibitors and microlaryngeal surgery wherever necessary. In this article we are discussing the various symptoms, the fifty patients complained of, and how we are able to pinpoint the diagnosis and the modality we adopted with the facilities available, and also a brief review of literature.

Lipoma of the external ear with osseous metaplasia.

Lipoma with osseous metaplasia of the external ear is an uncommon and has not been reported so far in Medline search for 30 years. The diagnosis was confirmed only after excision biopsy of the lesion. We report this case for its rarity.

An unusual complication of Thyroid Surgery and its management.

Stricture oesophagus is an unusal complication of thyroid surgery. There is only one case of such nature recorded in literature, which shows that the surgeon who operated may not have had any previous experience of head and neck surgery. Locating the stricture was difficult, more so planning the treatment modality was problematic. Informed consent for oesophagectomy with gastric pull through was taken. However when we explored the neck the stricture was seen just below the level of pyriform sinus. It could be successfully excised without end to end anastomosis.

Arterio venous malformation with auricular hypertrophy.

We report a case of arterio-venous malformation (AYM) of the external ear with hypertrophy in a 25 years old male which had been stable for many years, only to expand following trauma, with occasional bleeding episodes. Surgical correction and plastic reconstruction without proximal ligation of the feeding arterial system was contemplated.

Giant Cervical Osteophytes Their Significance in ENT Practice.

Foresteir's disease or Diffuse idiopathic skeletal hyperostosis (DISH) involving the cervical vertebrae in two patients is being presented as an uncommon cause of snoring and dysphagia. The radiological features of the giant osteophytes involving the cervical vertebrae are detected on routine skiagrams of the neck. A review of literature over ten years showed no such record of such a lesion occurring in C1-C2 vertebrae, whereas the occurrence in the lower cervical vertebrae is occasionally seen causing dysphagia. The relative merits of the surgical approaches are discussed.

Malignant pleomorphic fibrous histiocytoma of the larynx. A case report with review of literature.

A rare case of malignant pleomorphic fibrous histiocytoma of the larynx in a 40-year-old male patient is reported, with a review of the literature. This paper is a further contribution to the knowledge of rare tumours of the larynx. Radical surgery, as adopted in this case, is an accepted procedure.

Epidermolysis bullosa and its E.N.T. manifestations. Two case reports.

The present paper describes two rare cases of epidermolysis bullosa dystrophica (recessive), one with oesophageal stricture and another with laryngeal stenosis, along with other usual features of the disease. Different views on the line of treatment of the oesophageal stricture as a complication of this dreadful disease are discussed. Replacement of the strictured oesophagus by coloplasty may be contemplated in the first case, if the patient develops increasing dysphagia. In the second case, with cicatrical stenosis of the larynx and hoarseness of voice which is a rare complication of the disease, not reported in the literature so far, a tracheostomy is contemplated when the child develops acute respiratory distress. These two cases are under observation.