RESUMO
CASO CLÍNICO: Varón de 21 años con historia de exoftalmos izquierdo y diplopía de 2 semanas de evolución. La resonancia magnética mostró una lesión muy vascularizada etmoido-orbitaria con invasión de base del cráneo anterior y extensión orbitaria. La biopsia etmoidal confirmó un tejido fibrovascular compatible con angiofibroma. DISCUSIÓN: El angiofibroma nasofaríngeo juvenil (ANJ) es un tumor benigno con características locales de malignidad debido a su capacidad de invadir áreas adyacentes. En nuestro caso, el comienzo se presenta con manifestaciones de extensión orbitaria. Consideramos necesario un conocimiento amplio y un abordaje multidisciplinario con el fin de mejorar el pronóstico
CLINICAL CASE: The case is presented of a 21 year-old male with a history of left proptosis and diplopia of two weeks of onset. The MRI showed an ethmoid-orbital vascular lesion with anterior skull base invasion and orbital extension. Biopsy of the ethmoid confirmed fibrovascular tissue, which supported the diagnosis of angiofibroma. DISCUSSION: It is a benign neoplasm with local characteristics of malignancy due to its ability to invade adjacent areas. In this case, the debut presented with manifestations of orbital extension. A broad and multidisciplinary approach is needed in order to improve prognosis
Assuntos
Humanos , Masculino , Adulto Jovem , Angiofibroma/induzido quimicamente , Angiofibroma/patologia , Neoplasias Nasofaríngeas/induzido quimicamente , Neoplasias Nasofaríngeas/patologia , Neoplasias Oculares/tratamento farmacológico , Neoplasias Oculares/radioterapia , Exoftalmia/congênito , Exoftalmia/metabolismo , Neoplasias de Cabeça e Pescoço/diagnóstico , Angiofibroma/diagnóstico , Angiofibroma/prevenção & controle , Neoplasias Nasofaríngeas/diagnóstico , Neoplasias Nasofaríngeas/metabolismo , Neoplasias Oculares/complicações , Neoplasias Oculares/cirurgia , Exoftalmia/complicações , Exoftalmia/cirurgia , Neoplasias de Cabeça e Pescoço/tratamento farmacológicoRESUMO
CLINICAL CASE: The case is presented of a 21 year-old male with a history of left proptosis and diplopia of two weeks of onset. The MRI showed an ethmoid-orbital vascular lesion with anterior skull base invasion and orbital extension. Biopsy of the ethmoid confirmed fibrovascular tissue, which supported the diagnosis of angiofibroma. DISCUSSION: It is a benign neoplasm with local characteristics of malignancy due to its ability to invade adjacent areas. In this case, the debut presented with manifestations of orbital extension. A broad and multidisciplinary approach is needed in order to improve prognosis.
Assuntos
Angiofibroma/patologia , Neoplasias Nasofaríngeas/patologia , Órbita/patologia , Angiofibroma/diagnóstico por imagem , Angiofibroma/radioterapia , Angiofibroma/cirurgia , Biópsia , Angiografia Cerebral , Terapia Combinada , Diplopia/etiologia , Osso Etmoide/diagnóstico por imagem , Osso Etmoide/patologia , Exoftalmia/etiologia , Humanos , Imageamento por Ressonância Magnética , Masculino , Artéria Maxilar/diagnóstico por imagem , Neoplasias Nasofaríngeas/diagnóstico por imagem , Neoplasias Nasofaríngeas/radioterapia , Neoplasias Nasofaríngeas/cirurgia , Invasividade Neoplásica , Artéria Oftálmica/diagnóstico por imagem , Órbita/diagnóstico por imagem , Base do Crânio/diagnóstico por imagem , Base do Crânio/patologia , Adulto JovemRESUMO
Presentation of an uncommon form of distant primary dissemination of renal adenocarcinoma (RA) 5 years after radical surgery, the subcutaneous metastasis. The patient underwent surgical resection of metastasis, and later developed early pulmonary, mediastinal and new skin metastasis. A review is made of the incidence, therapeutical approach and prognostic value of skin metastasis due to RA.
Assuntos
Adenocarcinoma/secundário , Neoplasias Renais/patologia , Neoplasias Cutâneas/secundário , Adenocarcinoma/patologia , Adenocarcinoma/cirurgia , Humanos , Neoplasias Renais/cirurgia , Neoplasias Pulmonares/secundário , Metástase Linfática , Masculino , Neoplasias do Mediastino/secundário , Pessoa de Meia-Idade , Nefrectomia , Neoplasias Cutâneas/diagnóstico , Neoplasias Cutâneas/cirurgia , Tórax , Fatores de TempoRESUMO
Verrucous carcinoma includes approximately 5% of all neoplasias of the penis and is a tumoral variety of benign behaviour and differentiated histology. Our 10-case experience of penial verrucous carcinoma is reported here. In nearly all cases, partial penectomy was the definitive approach. No dissemination, locorregional or distant, was found in any of the report cases. Since prognosis of these tumours is good, we see no justification in performing lymphadenectomy, although it is advisable to adopt and expectant attitude when faced to inguinal adenopathies.
Assuntos
Carcinoma Verrucoso/patologia , Neoplasias Penianas/patologia , Idoso , Idoso de 80 Anos ou mais , Carcinoma Verrucoso/cirurgia , Humanos , Masculino , Pessoa de Meia-Idade , Neoplasias Penianas/cirurgiaRESUMO
We describe a patient with giant cell carcinoma with ectopic production of chorionic gonadotrophin hormone (CGH). This entity is compared with choriocarcinoma, given that the immunologic, histologic and chemical similarities between the two neoplasms can make their anatomic and pathologic differential diagnosis difficult. Clinical examination, response to treatment and CGH blood levels are the criteria for differentiation.
Assuntos
Carcinoma de Células Grandes/diagnóstico , Carcinoma de Células Grandes/metabolismo , Coriocarcinoma/diagnóstico , Gonadotropina Coriônica/metabolismo , Neoplasias Pulmonares/diagnóstico , Neoplasias Pulmonares/metabolismo , Carcinoma de Células Grandes/patologia , Carcinoma de Células Grandes/cirurgia , Quimioterapia Adjuvante , Diagnóstico Diferencial , Evolução Fatal , Humanos , Neoplasias Pulmonares/patologia , Neoplasias Pulmonares/cirurgia , Masculino , Pessoa de Meia-Idade , PneumonectomiaRESUMO
Cancer of scrotum is of interest, despite its relative infrequency, because of its historical importance (was the first known occupational cancer) and also of its aggressive behavior. We report a rare case of verrucous carcinoma in a 67 years old man, without recrudescence six months after surgical treatment.