1.
Pediatr Infect Dis J
; 28(3): 254-5, 2009 Mar.
Artigo
em Inglês
| MEDLINE
| ID: mdl-19209090
RESUMO
PFAPA syndrome (periodic fever, aphthous stomatitis, pharyngitis, adenitis) is a benign sporadic syndrome of unknown cause. We report 2 siblings diagnosed with this syndrome. The second case started crisis simultaneously with recurrence of crisis after a 3-year free interval in her brother. This temporal relation suggests environmental factor acting in genetically predisposed children.