RESUMO
We present a successful surgical repair of a rare variant of the common arterial trunk with unusual arrangement of the pulmonary arteries. The variant was not readily classified using either of the popular classifications for the common arterial trunk. It is appropriately described as a common arterial trunk showing aortic dominance, but with extrapericardial origin of the pulmonary arteries from the underside of the truncal arch. We also provide an account of cardiac development, which we suggest offers an accurate explanation for its morphogenesis.
Assuntos
Cardiopatias Congênitas , Persistência do Tronco Arterial , Humanos , Persistência do Tronco Arterial/cirurgia , Cardiopatias Congênitas/cirurgia , Tronco Arterial , MorfogêneseRESUMO
We present an alternative technique for the repair of a high partially anomalous pulmonary venous connection to the superior vena cava.
Assuntos
Veias Pulmonares , Veia Cava Superior , Humanos , Veias Pulmonares/anormalidades , Veias Pulmonares/cirurgia , Veia Cava Superior/anormalidades , Veia Cava Superior/cirurgiaRESUMO
Pseudocoarctation of the aorta is an uncommon congenital entity characterized by juxtaductal elongation and tortuosity of the aortic arch. It is known to be associated with aneurysm formation. Our patient is a 7.7-month-female infant followed prenatally by magnetic resonance imaging that detected this anomaly. Subsequently, postnatal preoperative computed tomography angiography was confirmatory. The operation comprised resection of the aneurysmal portion of the aorta and extended end-to-end reconstruction, without prosthesis usage. The left subclavian artery was reimplanted into the left carotid artery. The postoperative course was uneventful. Computed tomography aortography and transthoracic echocardiography demonstrated no residual stenosis at six months of follow-up.
Assuntos
Aneurisma da Aorta Torácica , Aneurisma Aórtico , Aorta Torácica/diagnóstico por imagem , Aorta Torácica/cirurgia , Aortografia , Feminino , Humanos , Lactente , Artéria Subclávia/diagnóstico por imagem , Artéria Subclávia/cirurgiaRESUMO
We present a patient with the extremely rare coexistence of two distinct coronary artery malformations: anomalous aortic origin of the right coronary artery from the left aortic sinus with intramural course and anomalous origin of the circumflex coronary artery from the right pulmonary artery. Surgical reimplantation of the anomalous left circumflex coronary artery to the aorta and unroofing of the intramural portion of the anomalous right coronary artery were performed.
Assuntos
Aorta Torácica/anormalidades , Anomalias dos Vasos Coronários/cirurgia , Vasos Coronários/cirurgia , Artéria Pulmonar/anormalidades , Seio Aórtico/anormalidades , Procedimentos Cirúrgicos Vasculares/métodos , Aorta Torácica/cirurgia , Angiografia Coronária , Anomalias dos Vasos Coronários/diagnóstico , Humanos , Lactente , Masculino , Artéria Pulmonar/cirurgia , Seio Aórtico/cirurgiaRESUMO
Origin of the circumflex coronary artery (Cx) from the pulmonary arteries is an extremely rare anomaly. We describe a two-month-old female patient with anomalous origin of the Cx from the right pulmonary artery associated with coarctation of the aorta. Reimplantation of the anomalous Cx to the aorta and coarctation repair were performed. There were no postoperative complications, and the patient was discharged in satisfactory condition.
