Case report - An acute presentation of lymphangiomatosis.

INTRODUCTION: Lymphangioma is an uncommon malformation of lymphatic system. Multiple colonic lymphangioma named as lymphangiomatosis is considered an extremely rare disease. PRESENTATION OF CASE: We report a case of colonic lymphangiomatosis presenting as recurrent right iliac fossa pain in a young female treated surgically. DISCUSSION: Lymphangiomatosis is a rare but benign disease with a variety of presentations. There are few reported cases in the literature at present and no guidelines regarding the diagnosis or treatment of the same. CONCLUSION: Our case demonstrates an unusual presentation of lymphangiomatosis treated surgically. Debate will remain on this rare condition.