RESUMO
Management of children with disorders of sexual differentiation (DSD) continues to cause questions and receive criticism. This review discusses some contradictions concerning the newly proposed terminology, nomenclature, and classification. Congenital adrenal hyperplasia (CAH) is the most common cause of DSD, and its management also remains controversial. Therefore, in this part of the article, we critically analyze available literature on gender identity, the need and timing of surgery in children with DSD and 46, XX karyotype.
Assuntos
Transtornos 46, XX do Desenvolvimento Sexual , Hiperplasia Suprarrenal Congênita , Identidade de Gênero , Diferenciação Sexual , Terminologia como Assunto , Transtornos 46, XX do Desenvolvimento Sexual/genética , Hiperplasia Suprarrenal Congênita/genética , Criança , Feminino , Humanos , Masculino , Diferenciação Sexual/genéticaRESUMO
Surgical management of children with disorders of sexual differentiation (DSD) is one of the most difficult problems in pediatric urology. In the second part of the article we continue to discuss the controversies concerning the surgical management of patients with the classical form of congenital adrenal hyperplasia and 46, XX karyotype - feminizing genitoplasty and its different types.