[Intra-abdominelle Lymphangiome]. / Intra-abdominal lymphangioma - Case Report.

Intra-abdominal lymphangiomas are very rare. We report the unusual case of a 4-year-old boy, who presented with acute abdominal symptoms due to intracystic hemorrhage following a blunt abdominal trauma. After the diagnostic management, the radical resection was done with a good outcome.

[A case report of prolonged hemolytic anemia in an infant due to a partial exchange transfusion]. / Prikaz slucaja protrahirane hemolizne anemije dojenceta zbog djelomicne ekssangvinotransfuzije.

An infant at the age of one month was admitted to hospital due to anaemia and icterus. Premature delivery was induced because of Rh immunisation. Newborn's grave condition permitted only one "blood volume" exchange transfusion and as a consequence prolonged haemolytic anaemia occurred. At the age of one month anti Rh-D antibody persisted in the infant circulation with the titre 1:16 in an indirect antiglobulin method.

[Results of the therapy of acute leukemia during 10 years (1972-1982)]. / Rezultat terapije akutnih leukemija kroz 10 godina (1972-1982).

The group of 31 patients with acute leukemia was analysed: 24 ALL and 5 ANLL. The complete remission was achieved in 84% of children. Mortality in induction was high and reached 16%. All recidives occurred with in 24 months from the diagnosis. 15% of patients achieve complete continuous remission (CCR) lasting 2 and more years, the result beeing better in patients treated with more intensive regimen. 53% patients will ALL achieved CCR for 5 and more years. In a small group of patients with ANLL the rate of CR is 60%. Only one girl, with a M 3 form lives more than 20 months.

[Case report of congenital deficiency of factor V and factor VIII]. / Prikaz slucaja kongenitalnog deficita F V i F VIII.

A case of a rare congenital combined deficiency of factor V (14%) and factor VIII (30%) is described for the first time in our literature. Nine years old girl was admitted to hospital because of nightly bleedings from hyperplastic and inflamed gums. Clinical picture was mild what is in accordance with the results of coagulation studies. Under substitution therapy tooth extraction passed without complications.

Brachial plexus palsy in neonates and children.

In 135 children with obstetrical palsy, clinical and electrodiagnostic studies on inital and serial evaluation aided in designing a conservative treatment program. Prevention of contractures, maintenance of muscle strength and reinforcing the child's awareness of the affected limb were predicated on the limiting factors of permanent denervation and agnosia. Instability of the scapula, scapulohumeral adhesions and elbow flexion with loss of active supination defy conventional range of motion exercises. Forced passive supination of the elbow may actually compound the problem of radial head dislocation and ulnar bowing. Because of the young age of most of the patients, only 7 have had orthopedic intervention. Rotational osteotomy of the humerus and transfer of intact muscles seem to improve function. Prior to selection of muscles for transfer, electromyography is advised. Later surgical treatment of the shoulder and elbow seems to improve cosmesis but not function. Of the 135 children, 70% had mild residua, 22% showed moderate impairment and 8% had severe deficit.

[Fanconi's anemia in 2 brothers]. / Fanconi anemija u dva brata.

Two cases of Fanconi anemia in brothers are described. Reticulocytosis and shortened survival of red blood cells in younger brother were observed. Ethiopathogenesis, therapy and prognosis are discussed.

Nerve conduction velocity determinations in juvenile diabetes: continuing study of 190 patients.

Few prospective studies on the concomitant finding of neuropathy in juvenile diabetics exist. An ongoing study of motor and sensory nerve conduction determinations in 190 diabetic children, with sequential studies in 108 of them over an eight-year period, is the subject of this report. The incidence of neuropathy in our sample population under five years of age is neglible. In the children over five years of age, 8% had abnormal nerve conduction velocity (NCV) of the peroneal nerve, 4.5% had abnormal median motor and sensory NCV on initial study. In the sequential studies of the children over five years of age, the percentage of abnormal NCV rose from 14% to 48% as the duration of diabetes increased from one year to more than five years. It is the older juvenile diabetics with the longest duration of diabetes who would appear to have the highest incidence of neuropathy.